Intestinal Hemangioma Research Articles

Hemangioma of the small intestine in a child

Small intestinal hemangiomas in surgical patients with diseases of the gastrointestinal tract occur in only 0.009% of cases. Intestinal bleeding is often the first and only sign of a disease that is asymptomatic for a long time. This pathology is also extremely difficult to diagnose.

Diagnostic Red Blood Cell Scintigraphy in GI Tract Bleeding From an Intestinal Hemangioma

Summary 99mTc‐labeled red blood cell (RBC) scintigraphy in vivo established the diagnosis of intestinal hemangioma in a 6‐year‐old girl suffering from gastrointestinal (GI) tract bleeding who had undergone an operation for removal of hemangioma at the nail bed. Other examinations, double‐contrast barium meal study and angiography, were unsuccessful in making the diagnosis. Intestinal hemangioma is rare in childhood, but a useful technique such as RBC scintigraphy should be performed to find the bleeding point of the GI tract, especially in case the patient has another obvious hemangioma.

Blue rubber‐bleb nevus syndrome with Masson's vegetant intravascular hemangioendothelioma

A 14-year-old Japanese male showed numerous small cutaneous hemangiomas and severe anemia produced by internal hemorrhages from intestinal hemangiomas. Histological studies revealed ectatic vessels lined by a single layer of endothelial cells. Six hemangiomas, with fibrous walls of variable thickness, showed characteristics of vegetant intravascular hemangioendothelioma (Masson) in an organizing thrombus. Electron microscopy confirmed that the dilated cavities, were lined by a layer of flattened endothelial cells, surrounded by a few pericytes and/or smooth muscle cells. No appreciable abnormalities were found in the blood vessels located in the clinically normal skin. A few amyloid deposits in the subepidermal connective tissue were also observed.

Disseminated neonatal hemangiomatosis: Successful hepatic resection with subsequent development of hydrocephalus

This is a report of an infant with cutaneous hemangiomas who underwent successful resection of an extensive hemangioma of the liver as well as multiple intestinal hemangiomas. Later, he developed hydrocephalus due to a cerebellar cystic hemangioblastoma. This case documents the usefulness of cranial computed tomography (CCT) in determining the extent of involvement in disseminated neonatal hemangiomatosis.

Intestinal hemangiomas and Maffucci's syndrome.

To the Editor.— To my knowledge, the association of Maffuci's syndrome and intestinal hemangiomas has not been previously recorded. One report from theArchivesdid describe hemangiomas of the hypopharynx, esophagus, ileum, and anal mucosa in a patient who the authors felt had both Maffucci's syndrome and the blue rubber bleb nevus syndrome (BRBN).1They ascribed the intestinal lesions to the BRBN syndrome. Because the vascular lesions in the BRBN syndrome are extremely variable and those in Maffucci's syndrome sometimes appear similar to the BRBN syndrome, I suspect their patient had a straightforward case of Maffucci's syndrome. I have recently seen a case of Maffucci's syndrome which supports this assumption. Report of a Case The patient was a 45-year-old white man who was admitted to the University of Washington Hospital for disarticulation of his right arm due to advanced chondrosarcomatous involvement. He had classical Maffucci's syndrome which had

Hemangioma of the Small Intestine With Gastrointestinal Bleeding

A 12-year-old boy had multiple hemangiomas of the small intestine. Severe chronic hypochromic microcytic anemia (iron deficiency anemia) with occult blood in the feces due to chronic blood loss was a presenting manifestation. Resection of individual hemangiomas at laparotomy resulted in cure of this condition. The possibility of intestinal hemangioma should be considered in the differential diagnosis of gastrointestinal hemorrhage and of intestinal obstruction. Exploratory laparotomy appears to be mandatory for the correct diagnosis and cure of the condition.

Surgical Implications of Intestinal Hemangiomas

The possibility of intestinal hemangiomas should be considered in every case of occult gastrointestinal bleeding.Intestinal hemangiomas are not always observed in association with hemangiomas of the skin. In addition to hemorrhage and the occasional mechanical obstruction, various gastrointestinal symptoms may occur. X-ray demonstration of phleboliths, constrictions or indentations in the bowel wall of a hemorrhaging patient is valuable in diagnosis. Use of transmitted light is helpful in locating smaller lesions.Operation is indicated in the presence of severe hemorrhage or obstruction. Otherwise, treatment should be individualized.

Thrombocytopenia Associated with Intestinal Hemangioma in A Child

A rare form of thrombocytopenia is that associated with hemangioma in the intestinal tract. Although only 18 cases have been reported in the literature, the incidence is probably more common. Unless this association is suspected, the opportunity for cure by surgery, as in the present case, may be lost. In addition to thrombocytopenia the presence of an intestinal hemangioma may be revealed by melena, gross hemorrhage or other gastrointestinal symptoms. The previous case reports are summarized and the differential diagnosis is discussed. In all similar cases reported in the literature, the thrombocytopenia has been cured after surgical removal of the hemangioma or its treatment by irradiation.