Pulmonary sequestration is a congenital pulmonary malformation in which non-functioning lung tissue receives systemic arterial blood supply and does not communicate with the adjacent tracheobronchial tree. Sequestrations may have their own visceral pleural lining (extralobar type) or may be invested by the visceral pleura of the remaining functioning lung (intralobar type). 1 Lee E.Y. Dorkin H. Vargas S.O. Congenital pulmonary malformations in pediatric patients: review and update on etiology, classification, and imaging findings. Radiol Clin North Am. 2011; 49: 921-948 Abstract Full Text Full Text PDF PubMed Scopus (69) Google Scholar , 2 Rosado-de-Christenson M.L. Frazier A.A. Stocker J.T. et al. From the archives of the AFIP. Extralobar sequestration: radiologic–pathologic correlation. RadioGraphics. 1993; 13: 425-441 Crossref PubMed Scopus (89) Google Scholar Extralobar sequestration infarction secondary to torsion of its blood supply is very rare, with only six reported cases among paediatric patients. 3 Chen W. Wagner L. Boyd T. et al. Extralobar pulmonary sequestration presenting with torsion: a case report and review of literature. J Pediatr Surg. 2011; 46: 2025-2028 Abstract Full Text Full Text PDF PubMed Scopus (19) Google Scholar , 4 Huang E.Y. Monforte H.L. Shaul D.B. Extralobar pulmonary sequestration presenting with torsion. Pediatr Surg Int. 2004; 20: 218-220 Crossref PubMed Scopus (28) Google Scholar , 5 Lima M. Randi B. Gargano T. et al. Extralobar pulmonary sequestration presenting with torsion and associated hydrothorax. Eur J Pediatr Surg. 2010; 20: 208-210 Crossref PubMed Scopus (13) Google Scholar , 6 Mammen A. Myers N.A. Beasley S.W. Torsion and infarction of an extralobar pulmonary sequestration. Pediatr Surg Int. 1994; 9: 399-400 Crossref Scopus (7) Google Scholar , 7 Shah R. Carver T.W. Rivard D.C. Torsed pulmonary sequestration presenting as a painful chest mass. Pediatr Radiol. 2010; 40: 1434-1435 Crossref PubMed Scopus (17) Google Scholar , 8 Uchida D.A. Moore K.R. Wood K.E. et al. Infarction of an extralobar pulmonary sequestration in a young child: diagnosis and excision by video-assisted thoracoscopy. J Laparoendosc Adv Surg Tech A. 2010; 20: 399-401 Crossref PubMed Scopus (12) Google Scholar Infrequently, extralobar sequestration may calcify. 9 Baker E.L. Gore R.M. Moss A.A. Retroperitoneal pulmonary sequestration: computed tomographic findings. AJR Am J Roentgenol. 1982; 138: 956-957 Crossref PubMed Scopus (10) Google Scholar Herein, we report a thoracic paraspinal torsed extralobar sequestration containing calcification, an entity that, to the authors' knowledge, has not been previously described.