Abstract
Congenital Pulmonary Malformations (CPMs) are a group of rare lung abnormalities affecting the airways, parenchyma, and vasculature. They represent a spectrum of abnormal development rather than discrete pathological entities. They are caused by aberrant embryological lung development which occurs at different stages of intrauterine life.
Highlights
With improved resolution of foetal sonography and Doppler studies, many of these lesions are detected “in utero.” eir natural history can be quite variable
The lesion of Congenital pulmonary airway malformation (CPAM) is characterised by solid adenomatous areas, which consist of closely packed tubular structures resembling terminal bronchioles without mature alveoli [1]. ese areas closely resemble normal foetal lung at 16-week gestation [2]
Prevalence rate of 1 per Newborns with large cysts can develop Surgery is recommended in Typically presented during respiratory distress, cyanosis, and feeding all cases
Summary
CPMs are a group of rare lung abnormalities affecting the airways, parenchyma, and vasculature. ey represent a spectrum of abnormal development rather than discrete pathological entities. ey are caused by aberrant embryological lung development which occurs at different stages of intrauterine life. CPMs are a group of rare lung abnormalities affecting the airways, parenchyma, and vasculature. E presentation, natural history, diagnosis and management of congenital pulmonary airway malformation, congenital lobar emphysema, pulmonary sequestration, bronchogenic cyst, and pleuropulmonary blastoma will be discussed. Ese areas closely resemble normal foetal lung at 16-week gestation [2]. The lesion of CPAM is characterised by solid adenomatous areas, which consist of closely packed tubular structures resembling terminal bronchioles without mature alveoli [1]. Interspersed with these adenomatous areas are cysts.
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