Pulmonary sequestration presented as massive left hemothorax and associated with primary lung sarcoma

Filomena Napolitano,Alfredo Garzi,Chiara Carlomagno,Mario Vitale,Vincenzo Di Crescenzo,Paolo Laperuta

doi:10.1186/1471-2482-13-s2-s34

Filomena Napolitano, Alfredo Garzi + Show 4 more

Open Access

https://doi.org/10.1186/1471-2482-13-s2-s34

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Abstract

Pulmonary sequestration is an uncommon disease, accounting for only approximately 1.5% of all congenital pulmonary malformations. In most cases, the diagnosis is a result of accidental radiological findings; it is rarely accompanied by clinical symptoms, and is more commonly associated with other congenital malformations. Herein, we reported a case of pulmonary sequestration presented as massive left hemothorax and associated with primary lung sarcoma. A pneumonectomy via thoracotomy was attended with complete resection of sequestration and of sarcoma. The postoperative course was unremarkable, and the patient was discharged on postoperative day 11.

Highlights

Pulmonary sequestration is an uncommon disease, accounting for only approximately 1.5% of all congenital pulmonary malformations
The diagnosis is a result of accidental radiological findings; it is rarely accompanied by clinical symptoms, and is more commonly associated with other congenital malformations
Pulmonary sequestration is defined as a mass of nonfunctioning lung tissue that receives blood supply from an anomalous systemic artery and does not communicate with the normal bronchial tree, being divided into two forms: intralobar sequestration (ILS) and extralobar sequestration (ELS) [1,2,3] Whereas ELS is enclosed within its own pleural membrane, ILS shares the pleural membrane of the normal lung

Summary

Introduction

Pulmonary sequestration is an uncommon disease, accounting for only approximately 1.5% of all congenital pulmonary malformations. The diagnosis is a result of accidental radiological findings; it is rarely accompanied by clinical symptoms, and is more commonly associated with other congenital malformations. In the present case pulmonary sequestration presented as massive left hemothorax was associated with primary lung sarcoma.

Results

Conclusion