Brugada Syndrome (BrS) is a channelopathy classified as a primary electrical disorder that has been a subject of study in the past three decades because of its association with cases of Sudden Cardiac Death (SCD) in young, asymptomatic, and apparently healthy patients. The typical manifestations are syncope and cardiac arrest accompanied by characteristic electrocardiographic patterns. In the latest advances to understand this syndrome, it has been identified genes and multiple mutations that have allowed the elaboration of hypotheses related to repolarization and depolarization which aim to explain the physiopathological mechanisms. In this article, a case of a 32-year-old man with no history of cardiovascular disease who debuted with syncope and electrocardiographic changes in the right precordial leads suggestive of type II and type I Brugada pattern (after ajmaline test), is presented. Also, a review of the literature is carried out in terms of definition, classification, pathophysiology, genetics, prognosis and treatment for this entity.