Purposes: To evaluate the diagnostic, treatment and prognosis aspects of the dermatofibrosarcoma protuberans at Joliot Curie Cancer Center in Dakar. Patients and Methods: It was about a retrospective and descriptive study led over a period of 11 years, from January 2000 till December 2010. It concerned 13 patients with a histological diagnosis of dermatofibrosarcoma protuberans who underwent surgery and follow up. Results: We found 13 cases of DFSP on a duration of 11 years. The sex ratio was 1,16. The average age was of 38,4 years. The diagnosis of DFSP was often late with an average deadline of 4,96 years. Tumor was protuberant and nodular for 12 patients (92,3%). The trunk was the most common location of the tumor. The average size was of 22 mm with extrems of 8 and 250 mm. we found 1 case of vertebral extension and 1 case of lung metastasis after sarcomatous transformation. Surgery was the first therapeutic way. A normally covered wound was obtained for 9 patients (69%). For the other cases one skin graft and two rotation-advancement flaps was useful for wound cover. Adjuvant radiotherapy was made for bone extension for 1 patient. Imatinib systemic therapy was ineffective for the treatment of vertebral extension and lung metastasis. Recurrence occurred for 4 patients (30,7%) after 4,7 years follow up and 1 patient died. Keywords: dermatofibrosarcoma protuberans; surgery; recurrence; sarcomatous transformation