Degos disease, or atrophic papulosis, is a rare chronic occlusive microvasculopathy with an unknown pathogenesis. To date, the disease is divided into a benign, long-term, skin form, and a malignant systemic form with damage to the organs of the gastrointestinal tract and central nervous system, which is accompanied by a high risk of death. The described clinical case of a man with a benign cutaneous form of Degos disease demonstrates a rare variant of the disease with erosive and ulcerative lesions of the penis. The skin process on the trunk and extremities is represented by typical pale pink papules with atrophic scars in the center, as well as erosions and ulcers on the skin of the penis. During the follow-up, the patient developed thrombosis and gangrene of the small intestine, which may indicate the systematization or malignancy of Degos disease. To date, you continue to observe the patient.