M.L.. 47-47-68, was born on 1 l/30/62 and passed meconium at birth. No external anal opening or tistula were seen. Examination under anesthesia revealed a rectal fistula entering the postertor wall of the vagina at the level of the cervix. A sigmoid end colostomy was performed. The distal rectum was oversewn and returned to the peritoneal cavity. During the first week of life, an intravenous pyelogram revealed congenital absence of the right kidney uith a normal-appearing left upper urinary tract. A cystourethogram performed at this time revealed a large bladder with low pressure left ureteral reflux: there was mild dilation of the ureter and calices. At 9 mo of age. an abdominoperineal pull-through procedure was carried out. At this operation it was noted that the patient had a complete duplication of the uterus. Each uterus had a single fallopian tube and a single ovary. At I I mo of age, she was readmitted to the hospital for correction of an anal stricture at the mucocutaneous junction by means of bilateral “V plastics.” The patient’s diapers were noted to be constantly wet and she had a chronic lower urinary tract infection that was treated with the approprtate antibiotics, She was watched in a conservative f;lshion for the anticipated appearance of urinary continence. By 5 yr of age, she was noted to be almost completely incontinent of urine. She underwent cystourethrogram and intravenous pyelogram annually and during thtr period of time, there was no change in her upper urinary tract. nor in the degree of retlux. Because of the persistence of the urinary incontinence and because urcthroscopy revealed a short patulous urethra, it was decided to perform a Young-Dees urethroplasty and left ureteroneocystostomy. This procedure was carried out on 3/15/67 without dihiculty. Postoperatively. the patient continued to be incontinent and displayed low pressure left ureteral reflux by cystogram. The patient was followed carefully and one year later. on 3/13/68. while still demonstrating low pressure reflux, she underwent exploration of the left ureter with the hope of performing another Young-Dees urethroplasty and ureteroneocystostomy. After dissecting out the ureter. it was obvious that the distal one-third was too scarred and fibrous to permit a successful uretero neocystostomy. She, therefore, underwent a left ureteral cutaneous anastomosis. Microscopic examination of the distal ureter revealed fibrosis and chronic inflammation, She had an uncventful postoperative recovery and was discharged. She was seen annually through April of 1973. The last intravenous pyelogram on J/26/73, revealed a normal appearing left upper urinary tract with no ureteral obstruction. It was noted at this ttmr that the patient cared for her uretcrostomy apphance herself without any difficulty. She stimulated a daily bo*rl movement by means ol a minienema using an all rubber ear syringe. At age I2 yr, she experienced menarche and each menstrual period was accompanied by such srvcre pain that she had to remain in bed and take large amounts of aspirin and codeine uith only partial relief of pain. After one year. the patient was seen by her pediatrician \nho made the diagnosis of urinary tract infection. Examination revealed a well formed left uretcrostomy that drained without obstruction into a urinary collecting bag. There was a large obvtoua right lower quadrant mass. This was easily palpable. stony-hard and projected above the level of the abdomen when the child lay flat. A No. 12 Coude catheter was passed into the bladder with ease. The bladder was found to be empty and irrigated clear. An intravenous pyelogram revealed a normally-functioning left uppet
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