Introduction . Hemichorea-hemiballismus (HCHB) is characterized by unilateral, brief, unpredictable involuntary movements of one body side. Methods . Three patients with HCHB complaints with hyperglycemia in the early symptoms of acute ischemic stroke were collected. Results . Three cases of sudden-onset hemichorea-hemiballismus movements of the upper and lower extremities were reported. First: Male, 63, uncontrolled movements in his right arm and leg worsened over time with a history of type 2 diabetes mellitus, uncontrolled for 10 years with the same history of DM in his family. The serum glucose level was 450 mg/dL, with 10.8% HbA1c, 3+ urine glucose and negative urine ketone. CT brain showed infarction of left basal ganglia. Second: Male, 51, involuntary movements in his left arm and leg for 13 days before admitted to the hospital. Serum glucose levels at the beginning of the disorder were 455 mg/dL with negative urine ketone. Head MRI showed hyperacute infarction in the right basal ganglia and right caudate nucleus. Third: Male, 44, with past history of uncontrolled DM, coming with involuntary movements in his right arm and leg occurring suddenly 4 h while driving a car. The serum glucose level at the beginning of the disorder was 264 mg/dl and negative urine. Head CT scan showed infarction of the left basal ganglia. Conclusion . The combination of new striatal lesions and hyperglycemia is related to the appearance of unilateral hyperkinetic movement disorders in patients. When hyperglycemia is detected and managed, movement disorders disappear within a few days and may not require symptomatic therapy with dopamine receptor antagonists.