A 72-year-old female patient attended the dental office with a complaint of tongue lesion and a time course of 3 months. At the physical examination, a nodular lesion was found, located on the back of the tongue, with mucosa-like staining, firm consistency, sessile implantation, measuring approximately 1.5 cm. Considering the clinical findings, the diagnostic hypothesis was granular cell tumor, and the excisional biopsy performed. The histopathological examination showed regions of cartilaginous matrix and newly deposited bone matrix without cellular alterations and the diagnosis of choristoma was established. The choristoma is a growth like a tumor, exhibiting microscopically normal tissue in an abnormal location. They are benign and rare lesions, showing great predilection for the tongue, mainly posterior region in 85% of the cases. In 70% of cases of oral choristoma the patients are female. A 72-year-old female patient attended the dental office with a complaint of tongue lesion and a time course of 3 months. At the physical examination, a nodular lesion was found, located on the back of the tongue, with mucosa-like staining, firm consistency, sessile implantation, measuring approximately 1.5 cm. Considering the clinical findings, the diagnostic hypothesis was granular cell tumor, and the excisional biopsy performed. The histopathological examination showed regions of cartilaginous matrix and newly deposited bone matrix without cellular alterations and the diagnosis of choristoma was established. The choristoma is a growth like a tumor, exhibiting microscopically normal tissue in an abnormal location. They are benign and rare lesions, showing great predilection for the tongue, mainly posterior region in 85% of the cases. In 70% of cases of oral choristoma the patients are female.