Congenital anomalies of the stomach are equally varied and infrequent. They may be discovered either by prenatal ultrasound investigations, or later during adulthood for those moderately or not obstructive, and without inflammatory involvement. Gastric duplications are the least frequent of all duplications of the alimentary tract; pyloric atresia and its variants are usually symptomatic at birth as soon as feeding is initiated. Asymptomatic aberrant pancreatic islets are quite commonly found at laparotomy, but when next to the pylorus, they may cause obstructive symptoms. As for gastric diverticulae, some should not be considered as within limits of a pathological condition; they are anyway more frequently encountered in adults.