A 52-year-old Japanese female was pointed out a pancreas tumor at healthy check and admitted to our hospital for further diagnosis and treatment on May, 1996. No apparent abnormality was found at physical examinations. She had anemia (Hb 8.9g/dl) which was recovered before surgical operation. Other laboratory data such as blood chemistry, hormonal examinations and tumor markers were within normal limits. Abdominal ultrasound and endoscopic ultrasonography revealed an 4cm in size, which showed slightly hypoechoic internal echo and anechoic cystic area. Magnetic resonance cholangiopancreaticography (MRCP) revealed a high-intensity tumor which compressed extrahepatic distal bile duct and main pancreatic duct. Abdominal angiography showed a hypervascular tumor which was feeded by mainly inferior pancreaticoduodenal artery and partially anterior superior pancreaticoduodenal artery. And finally she was suspected solid and cystic tumor (SCT) or non-functional islet tumor and was removed the tumor which was 5.0×3.3×3.2cm in size with fibrous capsule. That tumor consisted of yellowish solid tumor with hemorrhage and degenerative cystic area. Microscopic examination showed cubic tumor cells with sheets, cystic and papillary formation. Immuno-histological staining for α1-antitrypsin and NSE were positive. And this tumor was diagnosed SCT histologically. 189 cases with SCT have been reported in Japan from 1979 to 1995 and we reviewed these cases.