Uterus didelphys associated with obstructed hemivagina and ipsilateral renal agenesis: MR findings in seven cases

Abstract

Although a specific syndrome of the uterus didelphys, obstructive hemivagina, and ipsilateral renal agenesis had been reported in gynecologic literatures, it is not familiar to radiologists. We introduce this syndrome with radiological, especially MR findings. Imaging findings and medical records of seven patients with this syndrome were retrospectively reviewed. MR clearly demonstrated uterus didelphys with obstructed hemivagina in six of the seven patients. A remaining one showed uterus didelphys with left-sided hematometra and hematosalpinx who had undergone vaginal septum incision prior to the MR. We could also recognize ipsilateral renal agenesis in all five patients, in whom renal areas were examined on MR. After vaginal septum resection, symptoms disappeared in six patients. We could observe the disappearance of the obstructive complications with MR in three patients. MR can do much for the early diagnosis and the prevention against further complications of this condition because it can demonstrate the müllerian duct anomaly complicated with obstructed hemivagina in detail and even ipsilateral renal agenesis.