Abstract

Introducción. La púrpura Henoch-Schönlein (PHS) es la forma más común de vasculitis en la infancia; esta se da en pequeños vasos sanguíneos y no es frecuente que genere complicaciones graves como la vasculitis bullosa, tal como sucedió en el caso que se presenta a continuación.Presentación del caso. Paciente masculino de cinco años con un cuadro clínico consistente en artralgias y aparición de lesiones purpúricas en miembros inferiores. Luego de ser diagnosticado con PHS, presentó lesiones bullosas, por lo que fue hospitalizado y se inició manejo analgésico y tópico; durante su estadía en el hospital se vigiló su función renal y, ya que no presentó otras complicaciones, se dio de alta.Conclusión. Las publicaciones disponibles sobre PHS sugieren que su presentación cutánea bullosa en pediatría no es frecuente y que no siempre se relaciona con un compromiso renal y/o gastrointestinal como la variante clásica; sin embargo, siempre debe vigilarse la función de estos sistemas sin importar la gravedad dérmica de esta vasculitis.

Highlights

  • Henoch Schönlein purpura (HSP) is the most common type of vasculitis in childhood

  • HSP affects small blood vessels, and it rarely leads to serious complications such as bullous small vessel vasculitis, as it occurred in the case presented here

  • The available literature on HSP suggests that its cutaneous bullous manifestation rarely occurs in pediatric population and that, unlike normal HSP cases, it is not always associated with renal and/or gastrointestinal involvement

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Summary

Introduction

Henoch-Schönlein purpura (HSP) is the most common form of vasculitis in childhood. It is an immunoglobulin A (IgA)-mediated disorder characterized by palpable small-vessel vasculitis. Non-erosive arthritis can occur without permanent deformity in the ankles, knees, and feet.[2] As for skin lesions, blisters are the least frequent and are found in about 5% of cases: Saulsbury[3] found 2 patients with hemorrhagic bullous lesions in a series of 100 patients This case report describes an atypical presentation of a skin condition in a patient treated at a tertiary pediatric hospital in Bogotá D.C., Colombia. The diagnosis of HSP was reconfirmed, and the patient was hospitalized given his symptoms, mainly a severe skin condition; laboratory tests were performed, and intravenous analgesia with opioids was adjusted. Subsequent kidney function tests were normal, so he was discharged

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