Postpartum Aortic Dissection and Pulmonary Embolism in a Patient with Marfan's Syndrome: A Rare and Difficult Clinical Scenario

Sheeza Imtiaz,Kamran Hameed,Muhammad Kashif Shazlee

doi:10.13189/ijccd.2018.060101

Abstract

Postpartum Aortic Dissection and Pulmonary Embolism in a Patient with Marfan's Syndrome: A Rare and Difficult Clinical Scenario

Highlights

Aortic dissection is a rare disease with estimated incidence of 2.9 per 100,000 person years in general population. [1, 2] and 2,000 patients per year in the United States, of whom 5.3% are women of reproductive age
We present a case of Stanford type A aortic dissection along with pulmonary embolism in a young patient with Marfan’s syndrome during postpartum period
[9] Literature review from 1988 to 2012 yielded that postpartum aortic dissection usually occurred between Day 1 and 42 after delivery and Pregnancy alone without underlying contributing risk factors and Marfan syndrome were the two main risk factors accounting for 44.4% and 40.7% of cases, respectively. [12]

Summary

Introduction

Aortic dissection is a rare disease with estimated incidence of 2.9 per 100,000 person years in general population. [1, 2] and 2,000 patients per year in the United States, of whom 5.3% are women of reproductive age. Aortic dissection is a rare disease with estimated incidence of 2.9 per 100,000 person years in general population. [1, 2] and 2,000 patients per year in the United States, of whom 5.3% are women of reproductive age. 14-50 % of the cases are associated with Marfan’s syndrome and 34-71% with hypertension. [3, 4] It is a complex clinical scenario, difficult to diagnose and difficult to treat, considering the survival of both mother and fetus. We present a case of Stanford type A aortic dissection along with pulmonary embolism in a young patient with Marfan’s syndrome during postpartum period

Case Report

Discussion

Findings

Conclusions

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