Double Chambered Right Ventricle with Small Ventricular Septal Defect: Detection and Evaluation by Color Doppler Echocardiography - A Rare Case Report

Abstract

Double-chambered right ventricle (DCRV) is a rare condition seen only in 0.5-2.0 % of all cases of congenital heart disease (CHD). 80-90 % of DCRV cases are associated with various other congenital heart defects. In particular, perimembranous large ventricular septal defect (VSD) is the most common anomaly associated with DCRV. Anomalous muscular bundle (AMB) typically divides the right ventricle (RV) into a proximal high pressure and distal low pressure chamber. This aberration is often diagnosed during childhood and adolescence. Here we are presenting an exceedingly rare case of asymptomatic DCRV in an adolescent female with a small perimembranous VSD. Keywords: Double Chambered Right Ventricle, small perimembranous VSD, DCRV in an adolescent, facial anomalies, cleft upper lip