Children with hereditary spherocytosis (HS) and gallstones (GS) sometimes require simultaneous splenectomy and cholecystectomy. To minimize invasiveness, laparoscopic procedures were attempted for two children with HS and GS. In this article, we demonstrate the procedure in a 12-year-old boy. Planning the position of the surgical ports and the operator's position, we were able to perform both procedures by using only five surgical ports. We used clips for hemostasis of the splenic vessels including the main splenic artery and vein and did not need to use a stapling instrument (Endo-GIA). The spleen was removed through a trocar wound using a plastic retrieval bag (Endocatch II) without enlarging the size of the wound. The duration of surgery was 4.5 h, and blood transfusion was not required. Postoperative pain control was needed for only 1 day. Gastrointestinal function recovered within 20 h. Based on safety, the fine postoperative recovery, and the cosmetic aspects, our procedure appears excellent for children with HS and GS.