Introduction: The occurrence of left-sided gallbladder in the absence of situs inversus is a rare congenital anomaly. It is characterized by a complex liver structural abnormalities, including the presence of a right-sided falciform ligament, atrophy or agenesis of segment 4, absence of extrahepatic bifurcation in some occasion and abnormal intrahepatic branching patterns of the portal vein. Method: case: A 34-year-old blood-type AB Rh+ son donated right lobe to his mother (blood type B Rh+) with B-viral hepatitis and hepatocellular carcinoma. Preoperative CT was performed, and left-sided gallbladder anomaly was found in the donor liver. 3D analysis using Synapse 3D revealed right sided umbilical ligament, intrahepatic bifurcation of the portal vein and a long common trunk of P2 and P3. Result: Intraoperatively, cholangiography was performed after cholecystectomy via cystic duct and findings identical to the MR cholangiography was obtained. After hanging, the hepatic transection plane was kept to the left of the falciform ligament to prevent damage to the main intrahepatic portal trunk, using CUSA. The main trunk of middle hepatic vein was left to the donor and the V5 and V8 were temporarily ligated with hemolock clips for later reconstruction during bench procedure. The liver transection was otherwise, uneventful and the right portal vein, right hepatic artery and right duct were ligated separately. After right hepatic vein ligation, the graft was procured with the falciform ligament, and flushed with cold HTK solution as in our standard practice. There was no complication in donor. The left portal vein showed no disturbance in flow. The graft showed excellent function and the recipient recovered successfully. Conclusion: We have shown that it is technically feasible to retrieve the right lobe liver grafts from living donor without complication.