Background: Sacrococcygeal teratomas [SCT] are derived from embryonic germ-cell layers and are mostly encountered in infants. In adults, this entity is extremely rare and always worrisome for malignancy. Methods: The authors present a case of a 42-year-old woman with the pathologic diagnosis of SCT. The clinical presentation, the histologic findings and the patients' clinical outcome are described. A review of the literature on SCT in adults is also presented. Results: In this patient, who had no evidence of recurrence after adequate resection, examination of the specimen showed mature SCT. Conclusion: Although rare in adults, SCT should be considered in the differential diagnosis of patients with a pelvic mass presenting with obstructive symptoms. Modern imaging techniques may be helpful to delineate the extent of the mass, and surgical removal is generally indicated at the time of detection. Sacrococcygeal mature teratoma is surgically curable if the lesion is completely resected. The presence of malignant transformation is associated with a less favorable outcome. SUMMARY The sacrococcygeal area is the most frequent site of teratoma in infancy. This tumor rarely presents in adulthood, and is confined mostly to the intrapelvic space. Most common are benign, also called mature teratomas. We report a case of adult saccroccocygeal teratoma treated in our hospital, and a literature overview.Introduction The sacrococcygeal area is the most frequent site of teratoma in infancy [ 1]. A female, rather than male, predominance exists [ 2, 3]. This tumor rarely presents in adulthood. Unlike teratomas in infants, which are externally visible in 90% of cases, sacrococcygeal teratomas in adults are confined mostly to the intrapelvic space [ 4]. Most common are benign,