Stenosis In Association Research Articles

Rheumatic mitral stenosis in association with parital anomalous pulmonary venous return.

An unusual case is presented, in which mitral stenosis was accompanied by a persistent left superior vena cava communicating through a venous channel with the left pulmonary veins. The pulmonary veins were normally connected to the left atrium, but, due to elevation of the left atrial pressure from the mitral valve lesion, pulmonary venous blood was directed up the left superior vena cava to reach the right atrium. Although from an anatomical viewpoint this did not constitute true anomalous pulmonary venous drainage, the condition behaved as such haemodynamically. It was only at operation that the diagnosis was firmly established, but after mitral valvotomy the abnormal venous channel was obliterated by simple ligation without incident.

ANOMALOUS PULMONARY VENOUS DRAINAGE ASSOCIATED WITH MITRAL STENOSIS. REPORT OF A CASE SUCCESSFULLY REPAIRED.

THE combination of a congenital malformation and an acquired valvular lesion in the same heart is uncommon. To our knowledge there are 10 reported cases of rheumatic mitral stenosis in association with partial anomalous pulmonary venous drainage (Table 1). Three of the 10 patients were found to have this combination only at post-mortem examination1 , 2; three were incorrectly diagnosed as Lutembacher's syndrome,3 , 4 and 1 was discovered to have anomalous pulmonary veins at the time of mitral valvotomy.5 In only 3 of the cases was an accurate diagnosis made,6 7 8 and in only 1 of the 10 patients was a successful total . . .

Supravalvular Aortic Stenosis in Association with Mental Retardation and a Certain Facial Appearance

Supravalvular Aortic Stenosis in Association with Mental Retardation and a Certain Facial Appearance

Supravalvular aortic stenosis in association with mental retardation and a certain facial appearance.

Four patients with supravalvular aortic stenosis are reported. In three of these patients a certain facial resemblance was striking, and these three patients were also mentally and physically retarded. The cases are very similar to the four cases recently reported in the literature. Supravalvular aortic stenosis in association with mental retardation and a certain facial appearance may constitute a previously unrecognized clinical syndrome. A systolic thrill and murmur most pronounced in the first right intercostal space and just below the clavicle, with an empty vascular pedicle on the roentgenogram, may be a clue to the clinical diagnosis of supravalvular aortic stenosis. Supravalvular aortic stenosis is best demonstrated by left ventriculography. A collateral circulation between the coronary arteries and the internal mammary artery has been shown in one patient.

Tricuspid stenosis in association with right ventricular hypertrophy and the coexistence of right-sided endocardial fibroelastosis

The purpose of this communication is to report a case of congenital heart anomaly in which the main pathologic findings were tricuspid stenosis, gross right ventricular hypertrophy with a diminutive cavity of the right ventricle and great enlargement of the left ventricle, pulmonary atresia with intact interventricular septum, an atrial septal defect, a patent ductus arteriosus, and a right-sided endocardial fibroelastosis. A similar gross malformation has been described by Glaboff, 1 Elster, 2 Williams, 3 Edwards and co-workers. 4 In none of the previous cases, however, was right-sided endocardial fibroelastosis mentioned. The presence of endocardial fibroelastosis in the present case may help in part to explain the rather obscure right ventricular hypertrophy or dilatation present in such cases. The endocardial fibroelastosis may well be a factor also in the causation of the pulmonary atresia and tricuspid stenosis.