Life-threatening complications may occur during pregnancy in patients with Turner syndrome (TS), such as eclampsia, gestational diabetes, cholestatic hepatitis or aortic dissection (AD). In France, a fatal AD occurred in 2 patients after oocyte donation (OD). Therefore, since 2019, our reference center created, on a quarterly basis, the first national multidisciplinary meeting evaluating the risk of a potential pregnancy in patients with TS. It involves physicians specialized in maternal-fetal medicine, gynaecologists, endocrinologists, imaging and cardiology specialists. Sixty-two cases have been evaluated. The patients’ median age at diagnosis of TS is 11 years (IQR: 8–15) and their median age at evaluation is 33 years (IQR: 29–36.7). Spontaneous menarche was present in 13/62 (21%) women. Primary ovarian insufficiency was present in 51/62 (82%) at a median age of 15 years (IQR: 14–17.2). A 45,X karyotype was observed in 16/62 (26%) of cases. Bicuspid aortic valve (BAV) was present in 16/62 cases (25.8%). The patients’ median aortic index was 16 mm/m2 (IQR: 15–18.9), evaluated with CMR and/or transthoracic echocardiography. A pregnancy has not been contraindicated in 42/62 (67.8%) of cases. The reasons for the refusal were a previous aortic replacement (6/20 patients) or a significant aortic dilatation (14/20 patients). The aortic index was above 25 mm/m2 in one patient. Mean aortic index was significantly higher in the contraindicated patients compared to the other patients: 19.5 mm/m2 (range: 15.6–26.2) vs. 15.6 mm/m2 (range: 11.4–22) (P < 0.001), respectively. Seven live births occurred at a median maternal age of 34.5 (IQR: 32.7–36.7): 3 were natural and 4 after OD. No cardiovascular events, including AD, were observed during pregnancy and in the population evaluated. Our preliminary results suggest that a multidisciplinary team meeting could improve the safety of pregnancy in women with TS.