Renal Lymphangiectasia Research Articles

Role of CT scan in diagnosis of renal lymphangiectasia: our single-center experience

Background: Renal lymphangiectasia is rarely reported benign renal disorder of lymphatic malformation. Though found incidentally; it presents with nonspecific symptoms and shows characteristic findings in radiological imaging studies.Aim: Here, we report eight patients with symptoms, laboratory and imaging findings compatible with renal lymphangiectasia. This report describes clinical and laboratory characteristics, treatment, Imaging findings and outcome of a series of patients with renal lymphangiectasia and reviews the literature.Methods and material: Eight patients (mean age 45 years, male:female ratio 3:1) from 1st January 2011 to 30th June 2016; showing renal lymphangiectasia as incidental finding on CT IVP were included in the series. Imaging and laboratory findings were reviewed. Two out of eight patients (25%) underwent aspiration of collection and laboratory findings confirmed the diagnosis of renal lymphangiectasia. Four out of eight patients (50%) did not undergo aspiration of fluid and were offered conservative treatment. Two out of eight patients (25%) were donors for renal transplantation who were managed conservatively.Results: Renal lymphangiectasia was diagnosed on CT IVP. In each case, where aspiration of collection fluid was offered, the laboratory diagnosis of renal lymphangiectasia was confirmed and patients were managed conservatively. However, large collection in one patient was relieved by percutaneous aspiration.Conclusions: Renal lymphangiectasia can be diagnosed with CT scan and confirmed by laboratory tests. As it may be confused with other cystic lesions of kidney; proper diagnosis and exclusion of other differentials can be effectively offered by CT scan IVP, which can avoid unnecessary invasive treatment options.

Renal lymphangiectasia: know it in order to diagnose it.

Renal lymphangiectasia: know it in order to diagnose it.

Bilateral renal lymphangiectasia-an unusual cause of abdominal distension and flank pain in a child.

Renal lymphangiectasia (RL, also known as renal lymphangiomatosis or renal lymphangioma or parapelvic lymphangiectasia) is an uncommon benign disorder characterized by dilatation of perirenal, peripelvic and intrarenal lymphatic channels secondary to obstruction (1,2). About five cases of this entity in pediatric age group have been illustrated in literature till date (3-7). Diagnosis is based on the characteristic radiological findings. An 11 years old male patient presented with the history of fatigue, progressively increasing abdominal distension and bilateral flank pain since last 2 months.

Renal lymphangiectasia: One disease, many names!

Renal lymphangiectasia: One disease, many names!

Isolated Renal Sinus Lymphangiectasia—Close Mimic of Pelviureteric Junction Obstruction and Hydronephrosis

Renal lymphangiectasia is a rare disorder which may present as perirenal or peripelvic collection. Isolated renal sinus lymphangiectasia is a close differential diagnosis for pelviureteric junction obstruction on ultrasound, but can be resolved without ambiguity using computed tomography and magnetic resonance imaging. Here we describe such a case where imaging helped avoid unnecessary confusion.

La lymphangiectasie rénale, un cas rare d’infiltration périrénale

Renal lymphangiectasia is a bilateral cystic infiltration of the perirenal and parapelvic space which is caused by the obstruction of the renal lymphatic tissue. To our knowledge only numbers have been reported in the literature. Renal lymphangiectasia usually asymptomatic and incidentally diagnosed has absolutely no effect on the patient outcome. Radiological imaging is typical so that the diagnosis does not need to be confirmed by a cyst punction. The lack of knowledge concerning renal lymphangiectasia make it usually confused with another cause of polycystic renal infiltration, such as the polycystic kidney disease. We report herein a case of renal lymphangiectasia diagnosed incidentally by an abdominal ultrasonography.

An unusual case of bilateral renal lymphangiectasia

Renal lymphangiectasia is a very rare benign disorder characterised by dilatation of the perirenal and peripelvic lymphatics. The condition is commonly misdiagnosed for othercystic lesions of the kidney such as polycystic kidneys. The diagnosis can be made with near-certainty if classical imaging findings are recognised. We report a case of bilateral renal lymphangiectasia, diagnosed on ultrasonography and computed tomography based on the typical imaging findings and the laboratory analysis of aspirated fluid. The patient was managed conservatively.

Renal lymphangiectasia presenting with hypertension and polycythemia

We report a very rare case of renal lymphangiectasia, an accumulation of lymph in the renal lymphatic system secondary to obstruction. Our patient presented to his family doctor for an annual check-up which resulted with high blood pressure and polycythemia. An ultrasound was performed and revealed a large right perirenal collection. A year later, a controlled abdominal computed tomography scan showed a progression and compression of perirenal collection on the right kidney, as well as apparition of a left perirenal collection. Percutaneous drainage of both collections was unsuccessful. Laparoscopy-guided marsupialisation was performed and successful. Blood pressure lowered to normal range without medication. The patient's hemoglobin level decreased within normal range after 3 additional phlebotomies postoperatively.

Computed Tomography (CT) in the diagnosis of Childhood Renal Lymphangiectasia

A 14-year-old male patient presented with a history of intermittent bilateral flank pain for 2-3 months. There was no history of any urinary complaints or trauma. Renal function test was normal. Computed tomography (CT) scan of the abdomen revealed bilateral perinephric and peripelvic fluid collections, which were almost symmetrical. A provisional diagnosis of bilateral renal lymphangiectasia was suggested which was confirmed by laboratory analysis of aspirated perinephric fluid. Renal lymphangiectasia is a very rare benign disorder of renal lymphatics. CT can noninvasively diagnose this condition resulting in early treatment and reduced morbidity.

Linfangiectasia renal unilateral: Caso clínico

Renal lymphangiectasia is a rare disorder characterized by the presence of cystic masses in renal parenchyma, renal sinus or perinephric space. This condition, congenital or acquired, is probably caused by an alteration of renal lymphatic drainage to retroperitoneal lymph ducts. We report a 48-year-old woman, who consulted in the emergency room due to left flank pain and microscopic hematuria. Blood pressure and renal function were normal. A CT scan showed a multilocular cystic mass in the left renal sinus without alterations in the renal parenchyma. Renal lymphangiomatosis was diagnosed. The pain subsided with analgesics and did not recur. Annual clinical and ultrasound follow-up was suggested.

Linfangiectasia renal: achado incidental em tomografia computadorizada multicorte e revisão da literatura

Linfangiectasia renal é uma condição rara, caracterizada por coleções parapiélicas e perirrenais, que pode progredir de assintomática para insuficiência renal crônica. É apresentado um caso de achado incidental em tomografia computadorizada de linfangiectasia renal bilateral em paciente assintomático, com descrição dos principais achados à luz dos métodos de imagem e ampla revisão da literatura.

Pediatric Renal Lymphangiectasia: Importance of Recognition and Accurate Renal Imaging

Renal lymphangiectasia is a rare diagnosis. It is also referred to as renal lymphangioma, renal lymphangiomatosis, peripelvic lymphangiectasia, renal peripelvic multicystic lymphangiectasia, and hygroma renale. The presentation varies, and the diagnosis depends on accurate radiologic interpretation. We present the radiologic images of a pediatric patient who was diagnosed with renal lymphangiectasia after being evaluated for suspected nonaccidental trauma to emphasize the importance of identifying this entity by the characteristic radiologic findings.

Hennekam lymphangiectasia syndrome

Hennekam lymphangiectasia syndrome is a rare disorder comprising of intestinal and renal lymphangiectasia, dysmorphic facial appearance and mental retardation. The facial features include hypertelorism with a wide, flat nasal bridge, epicanthic folds, small mouth and small ears. We describe a case of a multigravida with bad obstetric history and characteristic facial and dental anomalies and bilateral renal lymphangiectasia. To our knowledge this is the first case of Hennekam lymphangiectasia syndrome with anodontia to be reported from India.

腎リンパ管拡張症に高レニン性高血圧症，成長ホルモン分泌不全性低身長症，多血症を伴った症例：６年間の経過報告

腎リンパ管拡張症の男児例について，6年間の経過を報告する。1歳11か月時に特徴的な画像所見から腎リンパ管拡張症と診断した。感染症罹患を契機に胸水・腹水が貯留するエピソードを繰り返していたが，当科での初診時以降は同様の胸腹水貯留はみられていない。画像所見上の腎周囲膜様構造物，腎盂周囲嚢胞に変化なく，エリスロポエチン高値および多血症は持続していた。経過中に成長ホルモン分泌不全性低身長症および高レニン性高血圧症が明らかとなり，それぞれ成長ホルモン補充療法，降圧療法を実施中である。本疾患は小児期に発症する嚢胞性腎疾患としては非常に稀で報告例も少なく，興味深い症例と考えられたので報告する。

Perinephric Fluid Collections Due to Renal Lymphangiectasia

Fluid collections around the kidneys on cross-sectional imaging may be caused by urine, blood, pus, lymph, or plasma. Ultrasonography (US), computed tomography (CT), and magnetic resonance imaging (MRI) can not only show and characterize the fluid, but also may help determine the underlying cause of the perinephric fluid collection, such as ureteric obstruction, kidney injury, infection, or renal lymphangiectasia. Renal lymphangiectasia is characterized by abnormal and ectatic lymphatic vessels within and around the kidneys. Dilated lymphatics may result in peripelvic cysts (intrarenal lymphangiectasia) and perinephric fluid collections (extrarenal lymphangiectasia), which can be visualized using US, CT, and MRI. Proper diagnosis on imaging helps in planning a conservative management approach to this benign condition, which requires intervention for only significant symptoms or complications. We describe a 60-year-old man with normal kidney function and bilateral perinephric fluid collections in whom renal lymphangiectasia was diagnosed noninvasively on the basis of characteristic findings on US, CT, and MRI.

Bilateral renal lymphangioma - An incidental finding

Renal lymphangiectasia is a very rare benign disorder of the renal lymphatics. It is known by many different names including renal lymphangiomatosis, parapelvic lymphangiectasia, hygroma renale and polycystic disease of the renal sinus.[1] The origin is unclear and it is generally regarded as a developmental malformation of the renal lymphatic system. It may be seen at any age. Familial association has been reported in some cases.[2] It can be confused clinically, radiologically, and surgically with autosomal dominant polycystic kidney disease in adults, and autosomal recessive polycystic disease in children. However, on imaging, these cysts are large, thin walled, parapelvic and central retroperitoneal in location. Renal parenchyma is relatively normal as against the other two conditions.[2] Clinically, it is usually asymptomatic and incidentally diagnosed.[1] The complications include hematuria, ascitis, occasional deterioration in renal function and rennin dependent hypertension.[3] The treatment of asymptomatic cases is not required. When collections are very large and causing pressure symptoms, percutaneous drainage may be carried out.[1] We report the case of a 28-year-old male patient who presented with mild dull aching pain abdomen for the past seven years. There was no other significant history in the past. An ultrasound was performed six years back with aspiration of approximately 20 ml fluid from the lesion for diagnostic purposes and he was diagnosed with renal lymphangioma. He was put on symptomatic treatment and asked to come for regular follow-up. During the present visit his renal functions were normal. Intravenous urography (IVP) revealed normal function bilaterally. However, the calyces were distorted [Figure 1]. Figure 1 IVU image taken at 15 minutes reveals distortion of calyceal outline Ultrasonography (USG) revealed multiple cysts in the perirenal and peripelvic location, on both sides, distorting the renal outline [Figure 2]. Figure 2 Axial USG image of the right kidney reveals multiple cysts in the perirenal region and the region of the pelvis Computed tomography (CT) and magnetic resonance imaging (MRI) revealed that the cysts were non-enhancing and were of cystic density on CT, [Figure 3] while they were of hypo-intermediate signal intensity on T1-weighted images and hyper intense on T2-weighted images [Figures ​[Figures44 and ​and5].5]. On no imaging modality was the parenchyma of the kidneys involved, however, it appeared markedly reduced in volume at the present visit. In view of the apparent parenchymal compromise, approximately 600 mL of chylous fluid was drained from both sides. The aspirated fluid was rich in protein and contained rennin. On microscopic examination only a few lymphocytes were seen, while no organism was isolated on culture of the fluid. Figure 3 Reformatted contrast enhanced coronal CT image reveals non enhancing extra-parenchymal hypo dense cysts in the perirenal region and the region of the pelvis of both the kidneys (more on the left side) causing distortion of the underlying parenchyma without ... Figure 4 Axial non-contrast enhanced T1-W MR scan at the level of the kidneys reveals that the cysts are of hypo-intermediate signal intensity Figure 5 Coronal T2-W MR scan at the level of kidneys reveals that the cysts are of hyper intense signal intensity We present this case to highlight the benign nature of this condition as against the conditions it can be confused with.

Renal lymphangiectasia presented by pleural effusion and ascites

A young male patient complaining of vague abdominal pain, dyspnea, generalized weakness and abdominal distension for 6 months was referred for abdominal ultrasound. Ultrasound showed enlarged echogenic kidneys, perinephric and renal sinus cystic fluid collections bilaterally with ascites and right pleural effusion. The ultrasound findings were confirmed by abdomen CT scan. Renal function test was within normal. Laboratory analysis of aspirated perinephric fluid revealed abundant lymphocytes. The radiological findings and perinephric fluid aspiration analysis are consistent with renal lymphangiectasia. Pleural effusion, in addition to ascites and perinephric fluid collections, is a new presentation of the disease. Ascites and pleural effusion were improved by diuretics.

Renal lymphangiectasia

Renal lymphangiectasia is an unusual benign anomaly. The case of a 34-year-old woman with bilateral renal lymphangiectasia is presented in this report. The nomenclature of this disease is confused in the literature. The possible aetiology of renal lymphangiectasia is discussed, along with its clinical manifestation, characteristics on ultrasonography, computed tomography and intravenous urography. The disease evolves slowly and usually needs no surgical treatment unless in an emergency.

Childhood renal lymphangiectasia

heterogenously hyperintense and hypointense on with a renal lymphangiectasia. At 2.5 years of followup, she remains asymptomatic without radiological change. Renal lymphangiectasia is a rare, benign tion of the perirenal lymphatic system. The lymphatic structures that surround the kidney fail to establish normal communication with the rest of the lymphatic system. The physiopathological process is ectasia of

Renal lymphangiectasia

Renal lymphangiectasia is a rare, benign, clinically non-specific disorder of uncertain origin, though most authors believe that it corresponds to a lymphatic obstruction. It is characterized by the presence of perirenal and/or peripelvic cystic areas that may be confused with renal cystic disease. Clinically, it may be asymptomatic or present as abdominal pain, hematuria or a palpable mass. Diagnosis can be made from findings on ultrasound and computerized tomography.