SPLENIC TORSION is a rare cause of abdominal mass in childhood. Its occurrence is sporadic and associated anomalies are infrequent. One previously reported infant had the prune belly syndrome.' We present a second case of splenic torsion in a patient with prune belly syndrome, which suggests that this association is not merely fortuitous. CASE REPORT A 15-month-old male infant with prune belly syndrome associated with urethral atresia and a patent urachus had required a cutaneous vesicostomy at birth because of urinary obstruction. He presented with a three-day history of fever, anorexia, constipation, irritability, and progressive mucosal evagination of the vesicostomy. Physical examination revealed a temperature of 38.5 ~ C, blood pressure 94/62 mm Hg, and heart rate 140/minute. He was markedly irritable and had a distended abdomen. The left posterolateral mucosal surface of the bladder evaginated through the vesicostomy. A smooth, firm, sharply demarcated, tender mass was palpated in the left lower quadrant distinct from the left kidney. There was no hepatomegaly and the spleen was not felt in its normal position. A digital examination of the rectum showed impacted stool but no distinct mass. The hematocrit was 37%, the WBC 13,900/mm', and there were increased platelets. No burr cells, Heinz bodies, or Howell-Jolly bodies were present. An intravenous pyelogram showed hydronephrosis and megaureters unchanged from previous studies. Barium enema showed impacted feces and medial displacement of the left colon. Ultrasonography of the abdomen demonstrated a 9 x 4 cm mixed solid and fluid mass. An exploratory celiotomy was performed. The spleen was located in the left lower quadrant. The normal supporting ligaments were absent and there was torsion of the spleen upon its vascular pedicle with evidence of infarction of the parenchyma. The pancreas was not involved and the distal pancreas was mobile rather than fixed to the retroperitoneum. Splenectomy was performed without difficulty and the patient had an uneventful postoperative course.
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