Quadricuspid Pulmonary Valve Research Articles

An Incidental Finding of Asymptomatic Quadricuspid Pulmonary Valve at Autopsy: A Case Report and Comprehensive Literature Review

An Incidental Finding of Asymptomatic Quadricuspid Pulmonary Valve at Autopsy: A Case Report and Comprehensive Literature Review

Quadricuspid pulmonary valve: A rare cause of pulmonary artery aneurysm.

A 17-year-old male presented to our hospital from an external center with complaints of chest pain and shortness of breath, referred with preliminary diagnoses of pulmonary stenosis and pulmonary artery dilation. Echocardiography revealed moderate pulmonary regurgitation and mild pulmonary stenosis. Coronary computed tomography (CT) angiography showed normal coronary arteries and no presence of a patent ductus arteriosus, but an aneurysmal dilation of up to 4 cm was observed in the pulmonary artery. The patient was found to have a quadricuspid (QPV) pulmonary valve, while the aortic valve appeared normal. No phenotypic anomalies or accompanying aortic or lung abnormalities were detected in this case. Our case represents the first in the pediatric age group diagnosed via CT scan. Our study contributes insights into the relationship between QPV anomaly and pulmonary artery aneurysm, aiding in the diagnosis and management of these rare conditions. Furthermore, our findings highlight the importance of evaluating the possibility of QPV in patients with pulmonary valve stenosis, regurgitation, or artery aneurysm, emphasizing the significance of coronary CT angiography in the diagnostic process.

Three-Dimensional Echocardiography: A Promising Tool for the Diagnosis of Quadricuspid Pulmonary Valve and Pulmonary Artery Aneurysm.

Three-Dimensional Echocardiography: A Promising Tool for the Diagnosis of Quadricuspid Pulmonary Valve and Pulmonary Artery Aneurysm.

Quadricuspid Pulmonary Valve with Pulmonary Artery Aneurysm.

HomeRadiologyRecently Published PreviousNext Reviews and CommentaryFree AccessImages in RadiologyQuadricuspid Pulmonary Valve with Pulmonary Artery AneurysmAyşe Füsun Bekirçavuşoğlu , Süleyman BekirçavuşoğluAyşe Füsun Bekirçavuşoğlu , Süleyman BekirçavuşoğluAuthor AffiliationsFrom the Bursa City Hospital, Doğanköy mah, 16110 Nilüfer, Bursa, Turkey.Address correspondence to A.F.B. (email: [email protected]).Ayşe Füsun Bekirçavuşoğlu Süleyman BekirçavuşoğluPublished Online:May 16 2023MoreSectionsPDF ToolsImage ViewerAdd to favoritesCiteTrack CitationsPermissionsReprints ShareShare onFacebookTwitterLinked In A 70-year-old female patient had repeatedly sought medical attention, and a subsequent chest radiograph showed enlargement in the pulmonary artery. Coronary CT angiography (CCTA) was performed, showing a quadricuspid pulmonary valve and aneurysmal enlargement of the pulmonary artery (diameter of 57 mm) (Figure). This was conservatively managed, and the patient is doing well.Images in a 70-year-old woman with multiple symptoms. (A) Chest radiograph shows an enlarged pulmonary artery (arrows). (B) Multiplanar reformatted coronary CT angiography (CCTA) scan shows a quadricuspid pulmonary valve (leaflets are numbered as 1, 2, 3, 4 [arrow]), with one smaller cusp (leaflet number 4). (C) Volume-rendered CCTA scan demonstrates aneurysmal dilatation of the pulmonary trunk and its main branches. Ao = aorta, LA = left atrium.Download as PowerPointOpen in Image Viewer The quadricuspid pulmonary valve is a rare congenital anomaly with a prevalence reported from one in 400 to one in 1000 in postmortem specimens (1). Although usually isolated, it may be associated with patent ductus arteriosus, atrial or ventricular septal defects, and aortic valve anomalies (2,3). Aneurysms of the pulmonary arteries are also rare, with a prevalence of 1:14000 in autopsy series (4). There are a limited number of cases associated with quadricuspid pulmonary valve (3–5). CCTA is a useful tool in the evaluation of rare anomalies that are difficult to evaluate with echocardiography.Disclosures of conflicts of interest: A.F.B. No relevant relationships. S.B. No relevant relationships.Data sharing: No data were generated or analyzed during the study.

Extremely severe quadricuspid pulmonary valve stenosis treated by percutaneous balloon valvuloplasty.

Extremely severe quadricuspid pulmonary valve stenosis treated by percutaneous balloon valvuloplasty.

Short-Axis Imaging of the Pulmonary Valve through a Modified Parasternal View

Background: The aortic and pulmonary valves are both tricuspid valves. All cusps of the aortic valve can be imaged in the parasternal short-axis view but the pulmonary valve cusps are not routinely imaged during trans-thoracic echocardiography. Methods: We evaluated the feasibility of imaging all three pulmonary valve cusps in the short-axis by a modified parasternal view in 100 consecutive children below the age of 5 years. Results: A satisfactory short-axis imaging of the pulmonary valve was possible in 96 of 100 consecutive children in whom a complete echocardiogram study was performed. This detected abnormalities in the pulmonary valve in 10 children. This included bicuspid pulmonary valves, tricuspid pulmonary valves with unequal cusps, and a quadricuspid pulmonary valve. Visualization of the pulmonary valve permitted preoperative planning of pulmonary valve repair in one infant with a concomitant large ventricular septal defect. Conclusion: An adequate visualisation of the pulmonary valve leaflets by a modified parasternal view during trans-thoracic echocardiography was feasible in a vast majority of young children. The modified pulmonary short-axis view should hence be included as the part of a comprehensive pediatric echocardiographic protocol.

Management of Giant Pulmonary Artery Aneurysm with Quadricuspid Valve Stenosis

AbstractThe pulmonary artery aneurysm (PAA) is a rare disease with no well-defined guidelines about the diagnostic criteria and its management. In fact, the indications for surgical treatment and the type of surgical approach are not clear. However, in case of giant PAAs with hypertension and pulmonary valve abnormalities, surgery should be considered as an effective and safe approach to prevent dissections or ruptures. In this report, we describe a successful case of surgical repair, using a Bioconduit with a pericardial patch to recreate the pulmonary artery bifurcation in a 72-year-old male with aneurysm of the pulmonary artery (max diameter: 72 mm), associated with quadricuspid pulmonary valve stenosis and pulmonary hypertension. The procedure was uncomplicated and the follow-up computed tomography scan at 4 months showed correct positioning of the graft with no sign of contrast leakage.

Rare congenital quadricuspid pulmonary valve stenosis evaluated by CMR

Rare congenital quadricuspid pulmonary valve stenosis evaluated by CMR

Surgical treatment for a pulmonary artery aneurysm with stenosis of the quadricuspid pulmonary valve.

We report a case of pulmonary artery aneurysm and pulmonary stenosis with a quadricuspid pulmonary valve in a 64-year-old woman. While pulmonary artery disease had been found as a child, she needed no treatment because of the absence of symptoms and her normal physical development. She began experiencing dyspnoea on exertion 3 years ago. Echocardiography showed pulmonary artery aneurysm and severe pulmonary stenosis with a quadricuspid valve. Computed tomography showed a pulmonary artery aneurysm extending from its main trunk to the bilateral branches. The pulmonary valve was replaced, and the pulmonary trunk and its bilateral branch were reconstructed. The patient's postoperative course was uneventful.

Coexistence of multiple congenital anomalies: quadricuspid pulmonary valve, infundibular pulmonary stenosis, coronary artery anomaly, biventricular hypertrophy, and short stature

A 67-year-old man was admitted to our hospital because of exertional dyspnea. The patient was short in stature, and a quadricuspid pulmonary valve (QCPV) and outflow stenosis at the infundibulum of the right ventricle, biventricular hypertrophy, and absence of the circumflex coronary artery were revealed by computed tomography (CT) and cardiac angiography. To our knowledge, the coexistence of these five conditions has not been previously reported. The patient has been placed on regular follow-up under beta-blocker therapy for ventricular hypertrophy and has not shown worsening symptoms for 2 years.

A rare combination of quadricuspid pulmonary valve.

A rare combination of quadricuspid pulmonary valve.

Quadricuspid Pulmonary Valve

Quadricuspid pulmonary valve (QPV) is a rare congenital cardiac malformation which is notable for its asymptomatic behavior. With only a few hundred cases reported in literature, its clinical significance is not exactly known, although many authors have placed its implications on the Ross procedure. We report a case of QPV which was detected on routine cardiac screening.

CT Findings of Quadricuspid Pulmonary Valve with Pulmonary Artery Aneurysm

CT Findings of Quadricuspid Pulmonary Valve with Pulmonary Artery Aneurysm

Quadricuspid Pulmonary Valve in a European Young Male Diagnosed by MRI

Quadricuspid Pulmonary Valve in a European Young Male Diagnosed by MRI

A Case Report of Quadricuspid Pulmonary Valve Identified by Transthoracic Echocardiography

A Case Report of Quadricuspid Pulmonary Valve Identified by Transthoracic Echocardiography

Giant pulmonary artery aneurysm and surgical repair

We present a 70-year old patient who had congenital quadricuspid pulmonary valve and a giant 8.2-cm pulmonary artery (PA) aneurysm who underwent successful surgical repair under normothermic, beating heart cardiopulmonary bypass. We utilize computed axial tomography with three-dimensional reconstructions to diagnose and follow these patients. This case highlights our perioperative management and technique of repairing giant PA aneurysms.

Quadricuspid pulmonary valve associated with atrial septal defects and pulmonary stenosis

A 1-month-old Hispanic female was referred to the cardiology service. During physical examination, a systolic ejection murmur at the pulmonic area was auscultated. The echocardiography evaluation of the pulmonary valve demonstrated a quadricuspid pulmonary valve (QPV) with slightly thickened leaflets, associated atrial septal defects and mild pulmonary stenosis. QPV is a rare congenital anomaly variant that can remain asymptomatic with few or non-hemodynamic alterations. Associations with structural or functional alterations have been reported. This is the first case of QPV that was diagnosed in a Hispanic newborn.

Quadricuspid pulmonary valve and left pulmonary artery aneurysm in an asymptomatic patient assessed by cardiovascular MRI

We present a coincidental finding of quadricuspid pulmonary valve and left pulmonary artery aneurysm. As both the pulmonary valve and the pulmonary trunk with its main branches are hard to visualise with cardiac ultrasound, most abnormalities described so far are from autopsy series. With the increasing use of CMR and its excellent potential for visualising both pulmonary valve and pulmonary arteries, we believe more cases will be discovered in the near future. Although pulmonary artery aneurysm are rare, timely detection may prevent lethal bleeding.Electronic supplementary materialThe online version of this article (doi:10.1007/s12471-011-0115-3) contains supplementary material, which is available to authorized users.

Quadricuspid Pulmonary Valve

Quadricuspid pulmonary valve (QPV) is a rare congenital cardiac entity. The recognition of QPV has clinical significance as it can cause pulmonary valve dysfunction. It is also important to recognize this condition in patients undergoing the Ross procedure. We report a case of QPV diagnosed by computed tomography with associated pulmonary stenosis and right ventricular hypertrophy.

Congenital Quadricuspid Pulmonary Valve in an Adult Patient with Double Valvular Lesions and Poststenotic Dilatation of the Trunk and the Left Branch of the Pulmonary Artery: A Case Presentation and Review of the Literature

The quadricuspid pulmonary valve (QPV) is a rare congenital anomaly reported in the general population. There are less than 300 reported cases in the literature to date. It has been found in one in 400 to one in 2000 autopsies. We describe here the case of a 47-year-old patient who presents with a QPV with double valvular lesions (stenosis and insufficiency), causing a poststenotic dilatation of the trunk and the left branch of the pulmonary artery (PA). The diagnosis was made by transesophageal echocardiography (TEE) and confirmed by tomographic angiography (computed tomography). The English as well as the Spanish literature were reviewed. To the best of our knowledge, this is the first case of: (1) congenital QPV with double valvular lesions (stenosis and insufficiency), complicated with (2) aneurysmatic dilatation of the PA trunk as well as left branch, and (3) diagnosed by a TEE.