Origin Of Right Pulmonary Artery Research Articles

Familial recurrence of anomalous origin of right pulmonary artery from the aorta

Familial recurrence of anomalous origin of right pulmonary artery from the aorta

One-stage repair of interrupted aortic arch, aortopulmonary window, and anomalous origin of right pulmonary artery with autologous tissues

Interruption of the aortic arch, distal aortopulmonary septal defect, and aortic origin of the right pulmonary artery with intact interventricular septum were associated findings in a 4-month-old infant who underwent successful one-stage repair without the use of any synthetic material, thus allowing for a potential for growth of both the pulmonary artery and the aorta. The baby made an uneventful recovery and remains asymptomatic 36 months after repair.

Use of autogenous aortic and main pulmonary artery flaps for repair of anomalous origin of the right pulmonary artery from the ascending aorta

in patients with origin of the right (RPA) or left pulmonary artery from the ascending aorta, the RPA or, much less commonly, the left pulmonary artery arises from the ascending aorta in the presence of separate aortic and pulmonary valves and without the interposition Of ductal tissue. 1" 2 The RPA usually originates from the right posterior aspect of the ascending aorta. 3 Physiologically, the alteration creates a large left-to-right shunt. The contralateral lung is therefore subjected to the entire right ventricular output in addition to flow contributed by associated anomalies, such as patent ductus arteriosus, aortopulmonary septal defect, atrial septal defect, or ventricular septal defect, which have been present in greater than 60% of previous reports. 1 4 Without early operation the natural history of this condition is dismal, with a mortality rate of approximately 70% at 6 months of age and 80% at I year of age. 5 Armer and associates 6 reported the first successful anatomic repair of anomalous origin of the RPA from the ascending aorta with interposition of a polyester fiber graft between the RPA and the main pulmonary artery (MPA). The first successful primary repair was reported by Kirkpatrick, Girod, and King. 7 Traditionally, primary repair is generally reserved for those patients in whom the RPA originates from the posterior aspect of the aorta in close proximity to the MPA. s When the RPA arises from the right lateral aspect of the aorta, the right hilum is often mobilized medially to allow apposition of the RPA and MPA without tension. Alternatively, an interposition synthetic graft is placed either anterior or posterior to the aorta 5, 9 We propose a modified native tissue repair that reduces tension on the RPA-MPA anastomosis. The ascending aorta, proximal aortic arch vessels, the MPA, and both branch pulmonary arteries are widely mobilized. As soon as cardiopulmonary bypass has been established, the RPA is temporarily clamped or snared. The patent ductus arteriosus, if present, is doubly ligated and divided. After crossclamping of the aorta, the anterior aortic circumference is incised transversely at the level of the RPA origin (Fig. 1). Under direct vision, the remaining aortic circumference is transected, with a generous cuff of posterior aortic wall left around the RPA origin (Fig. 2). Alternatively, the posteromedial aspect of the aortic wall can be left intact. Utmost care should be taken to avoid compromise of the left

Origin of the Right Pulmonary Artery from the Ascending Aorta: Longest Survivor Without Receiving Surgical Repair

We report a case of origin of the right pulmonary artery from the ascending aorta. Pulmonary arteriography showed an opacification of the enlarged left pulmonary artery without filling of the right pulmonary artery. Pressure study showed that the pulmonary systolic pressure was almost equal to the systemic pressure. The present case is characterized as the longest-term survivor in the literature with aortic origin of right pulmonary artery without receiving surgical repair.

Aortic origin of right pulmonary artery: early detection by cross-sectional and color-Doppler-echocardiography in two infants submitted to successful surgical repair

The aortic origin of the right pulmonary artery was recognized in two infants by cross-sectional echocardiography. The sub-costal short axis view was sufficient to make the diagnosis. The Doppler and color-Doppler techniques were useful in adding the hemodynamic information to the anatomical diagnosis. Early surgical correction was performed in the infants with success without needing to resort to cardiac catheterization.

A Successful Case of the Anomalous Origin of Right Pulmonary Artery from Ascending Aorta

A Successful Case of the Anomalous Origin of Right Pulmonary Artery from Ascending Aorta

Surgical Correction of Anomalous Origin of Right Pulmonary Artery From Ascending Aorta With Left Patent Ductus Arteriosus

Surgical Correction of Anomalous Origin of Right Pulmonary Artery From Ascending Aorta With Left Patent Ductus Arteriosus

Aortic Origin of Right Pulmonary Artery: Successful Surgical Correction in Three Consecutive Patients

Over a period of four years (1981 through 1984), 3 infants with aortic origin of the right pulmonary artery were seen in our surgical unit. Two infants had a persistent ductus arteriosus, which arose from the left subclavian artery in 1 of them who also had a right-sided aortic arch. There were no other associated abnormalities. Preoperative diagnosis was established by echocardiography in 2 infants. Anatomical surgical correction was undertaken in all 3 infants under cardiopulmonary bypass. There were no operative deaths. One child required reoperation at 15 months for anastomotic stenosis. All 3 children were well two to five years postoperatively with scintillographic evidence of normal ventilation and perfusion. Our experience indicates that this rare but severe congenital cardiac anomaly is easily diagnosed by echocardiography, and confirms that it is eminently amenable to surgical correction.

Cross-sectional and pulsed Doppler echocardiographic features of anomalous origin of right pulmonary artery from the ascending aorta

Cross-sectional and pulsed Doppler echocardiographic features of anomalous origin of right pulmonary artery from the ascending aorta

Similarity of anomalous origin of right pulmonary artery from the ascending aorta to d-transposition of the great arteries: 2D echographic and Doppler study

Explorations ultrasons d'un nouveau-ne de 1 jour qui presentait une origine de l'artere pulmonaire droite a partir de la paroi posterieure de l'aorte ascendante

１０ｍｍ導管を用いた７カ月乳児右肺動脈大動脈起始症の術後遠隔期血行動態

１０ｍｍ導管を用いた７カ月乳児右肺動脈大動脈起始症の術後遠隔期血行動態

A Case of Anomalous Origin of Right Pulmonary Artery from the Ascending Aorta

A Case of Anomalous Origin of Right Pulmonary Artery from the Ascending Aorta

Isolated aortic origin of right pulmonary artery: Report of a case with special reference to pulmonary vascular disease in the left and right lungs: S. Yamaki, Y. Suzuki, E. Ishizawa, et al. Chest 83:575–578, (March), 1983

Isolated aortic origin of right pulmonary artery: Report of a case with special reference to pulmonary vascular disease in the left and right lungs: S. Yamaki, Y. Suzuki, E. Ishizawa, et al. Chest 83:575–578, (March), 1983

Isolated Aortic Origin of Right Pulmonary Artery: Report of a Case with Special Reference to Pulmonary Vascular Disease in the Left and Right Lungs

Morphometric study of the pulmonary vasculature was performed on lung biopsy specimens from a one-year-old girl who underwent anatomic repair of isolated aortic origin of the right pulmonary artery. Medial hypertrophy of small pulmonary arteries in the right lung was much less remarkable than that in the left lung. In contrast, intimal lesions in the right lung were much more advanced than those in the left lung. Fully oxygenated blood in the right pulmonary artery might suppress medial hypertrophy in response to high pressure and thin media fail to protect intima from high pressure, resulting in severe intimal lesions. This situation in the right lung resembles that in complete transposition of the great arteries.

Isolated aortic origin of right pulmonary artery; Report of a case with special reference to pulmonary vascular disease

Isolated aortic origin of right pulmonary artery; Report of a case with special reference to pulmonary vascular disease

Scanning suprasternal echocardiography.

Scanning suprasternal echocardiography was performed in 280 patients with a variety of cardiac anomalies. By using the special suprasternal transducer on the suprasternal notch, the aortic arch, right pulmonary artery, and left atrium were recorded superoinferiorly. From this reference position various scanning techniques were made to record the main pulmonary artery, pulmonary valve, ascending aorta, aortic valve, and distal aortic arch, wherever possible. These scans made it possible to assess (a) the integrity and size of right pulmonary artery and main pulmonary artery in pulmonary atresia, stenosis of origin of right pulmonary artery, pulmonary artery banding, kinked Waterston anastomosis, and aneurysm of pulmonary artery; (b) relative positions of aortic valve and pulmonary valve in malposition complexes; (c) the position and size of the aortic arch in tetralogy of Fallot and aortic coarctation. Measurements of the left atrium made by suprasternal echocardiography were consistently larger than those made by praecordial echocardiography. Changes in relative sizes of aortic arch, right pulmonary artery, main pulmonary artery, and left atrium were also documented in the various cardiac anomalies. The atrial baffle after Mustard repair for d-transposition of the great arteries and the atrial membrane in cor triatriatum were also demonstrated. The introduction of scanning techniques has thus widened the scope of suprasternal echocardiography.

Double-outlet right ventricle with origin of right pulmonary artery from a right-sided ductus arteriosus

A patient with double-outlet right ventricle is reported with the heretofore unreported association of a right pulmonary artery arising from a persistent right ductus arteriosus. The patient also had an infracrista ventricular septal defect, a secundum atrial septal defect, severe bicuspid valvular pulmonary stenosis, and a right-sided aortic arch.

Origin of right pulmonary artery from ascending aorta.

A case is reported of a 20-day-old infant with origin of the right pulmonary artery from the ascending aorta. Besides its abnormal origin, the artery was stenotic in its proximal half. We believe the malformation results from persistence of the distal (instead of the proximal) part of the primitive sixth aortic arch and of a portion of the right dorsal aorta. The presence of ductal tissue in the wall of the right pulmonary artery supports this concept. The pulmonary vasculature in the two lungs showed great differences in medial and intimal characteristics. A second case of origin of the right pulmonary artery from the aorta, deseribed elsewhere, provided material for comparative study of the structure of the right main pulmonary arteries and the intrapulmonary branches.