The s imul taneous occurrence of gliomas in the cerebel lum and ce rebrum of the same ind iv idua l is rare. Of the possible mechan isms responsible, t h a t of mul t ip le p r imary tumours aris ing independen t ly has always failed to gain m u c h suppor t . Russel l and R u b i n s t e i n 9 poin ted ou t t h a t this concept would be more acceptable if i t were possible to demons t r a t e mult i focal benign cerebral as t rocytomas , b u t to the i r knowledge th is had never been es tabl ished; in the ma jo r i t y of cases repor ted the t umours were of so m a l i g n a n t a natu re t h a t the deposits could well be metas ta t i c . I n the case we describe a diffuse as t rocyt ic glioma of the ce rebrum and mesencephalon was accompanied b y nodules of glial t u m o u r in each of the cerebel lar hemispheres in a p a t i e n t wi th cut aneous yon Reck l inghausen ' s disease and bi lateral phaeochrome tumours of the adrenal medulla.