Multiple Supernumerary Teeth Research Articles

Cleidocranial dysplasia presenting with retained deciduous teeth and impacted permanent and supernumerary teeth

Cleidocranial dysplasia is a disease that occurs secondary to a dominant autosomal inheritance. There is no predilection for any genre or ethnic group. As there is a delay in the eruption and/or absence of permanent teeth, the patients usually report to a dental surgeon for replacement of the missing teeth. This condition is characterized by several cranial malformations and underdevelopment, absence of clavicles, and multiple impacted supernumerary and permanent teeth. The diagnosis of the condition is usually based on the presence of the above-mentioned main features and on clinical and familial evidence. Here we report a rare case of cleidocranial dysplasia in a male patient, having most of the characteristic features of this syndrome.

Management Of Multiple Impacted Supernumerary Teeth In A Non-Syndromic Patient Using Cone Beam CT

Supernumerary teeth can present in various forms and in any region of the mandible or maxilla, but have a predisposition for the anterior maxilla. They can cause a variety of complications in the developing dentition. The occurrence of multiple supernumerary teeth in a non syndromic patient is extremely rare and it becomes a difficult task when they remain impacted. Here we present a modified treatment plan and management of such a patient using CBCT.

다수의 과잉 소구치를 가진 정신지체 환자의 치험례

과잉 소구치는 장애 환자에서 교정적 문제를 일으켜 구강 위생 관리의 어려움을 초래할 수 있는데 발생 시기가 늦고 병리학적 문제의 발생 가능성이 낮으며 재발의 가능성이 높으므로 발거 시기를 전체 영구치열이 완전한 성숙을 이룬 후로 미루어야 하며 매복되어 있어 특이할 만한 합병증이 발견되지 않는 경우, 수술적 위험성을 감수하기보다는 남겨 두는 것을 추천한다. The supernumerary premolars account for 4%-9% of all supernumeraries and reported prevalence is 0.01%-1.00%. Multiple supernumerary teeth can be seen in syndromic phenotypes. But, only 2% of supernumerary premolars exhibited any pathological changes. Most of them cause interference with normal occlusal development that makes maintaining the disabled patients's oral hygiene difficult. It is recommended to delay the timing of extraction until the full permanent dentition is mature. If there is no complication, leaving the supernumerary premolars impacted is recommended. This case is about mental retardation patients with multiple supernumerary premolars.

Non-syndromic multiple impacted supernumerary teeth: two case reports

Multiple impacted teeth may be related to syndromes and metabolic disorders. In some cases, however, impaction of multiple teeth is not accompanied by any other disorder or syndrom. Hyperdontia or supernumerary teeth without associated syndromes is a rare phenomenon, as supernumerary teeth are usually associated with cleft lip and palate or other syndromes such as Gardeners syndrome, cleidocranial dysplasia and trichorhinophalangic syndrome. The aim of this paper is to demonstrate that asymptomatic multiple impacted ectopic teeth are not always associated with a syndrome or a disorder. A 15-year old male patient attended our clinic with a chief complaint of irregular teeth and unaesthetic smile. In intraoral examination irregular and amorphous erupted teeth were noticed. On routine radiographical examination, impacted supernumerary teeth were noticed in maxilla and mandible. A 37-year old male patient attended our clinic for routine examination and radiographic examination revealed supernumerary and amorphous teeth in mandible and maxilla. In our cases, medical and family history and extraoral examination were not suggestive of any syndrome or metabolic disorder. A general physician was consulted who confirmed that there was no associated syndrome. The supernumarary teeth were surgically extracted. The 15 year old patient who was suffering from irregular teeth was directed to orthodontics clinic. In conclusion, routine radiographic examination may reveal multiple impactions, even if there is no absence of teeth. The etiologic factor of multiple impacted supernumerary teeth is still not clearly known, especially in cases without any syndrome. However, additional examinations may be necessary to exclude systemic and metabolic conditions.

A Rare Combination of Aggressive Periodontitis with Multiple Impacted Supernumerary Teeth

A Rare Combination of Aggressive Periodontitis with Multiple Impacted Supernumerary Teeth

Teeth Erupted From the Buccal Mucosa: Simple Odontogenic Choristoma or Accessory Teeth?

The eruption of developed teeth from the buccal mucosa is a rare phenomenon in the head and neck region. Such phenomena are possibly choristomas, tumorlike masses of histologically normal tissue occurring in an abnormal position. However, the accurate classification of this abnormality remains debatable. This report describes a case of a congenital, maldevelopmental, and noncystic lesion in a 4-year-old girl without other anomalies. To the authors' knowledge, this is the first case of multiple supernumerary teeth forming in the buccal and zygomatic regions.

Clinical spectrum of cleidocranial dysplasia in a family with twins

Cleidocranial dysplasia (CCD) is a rare congenital defect of autosomal dominant inheritance, primarily affecting bones that undergo intra-membranous ossification. Herein is reported the case of monozygotic male 13-year-old twins with typical features of this syndrome, such as large wide-open fontanels, abnormal clavicles with narrow, sloping shoulders that can be apposed at the midline, short stature, mid-face hypoplasia, multiple supernumerary teeth, and skeletal anomalies. Their physical appearance led to the diagnosis of CCD. Genetic analysis found a C-T exchange in exon 2 at cDNA position 568, which changes the codon CGG for arginine to TGG for tryptophan (R190W) of the runt-related transcription factor 2 RUNX2 gene. CCD should be suspected in patients with persistence of the widely open anterior fontanels and sutures, short stature, and poor clavicles, calvarium, or teeth. Timely recognition and hereditary tendency counseling is required and useful because of the possibility of covert transmissibility and sporadic genetic mutation.

多数の埋伏過剰歯を伴った鎖骨頭蓋異骨症の1例-3D-CTの有用性-

多数の埋伏過剰歯を伴った鎖骨頭蓋異骨症の1例-3D-CTの有用性-

A 13-year-old caucasian boy with cleidocranial dysplasia: a case report

BackgroundCleidocranial dysplasia (CCD) is a rare congenital autosomal dominant skeletal disorder. The disorder is caused by heterozygosity of mutations in human RUNX2, which is present on the short arm of chromosome 6p21. The incidence of CCD is one per million births. CCD appears spontaneously with no apparent genetic cause in approximately 40% of affected patients, and one in three patients has unaffected parents. The most prevalent features associated with CCD are aplastic or hypoplastic clavicles, supernumerary teeth, failed eruption of permanent teeth, and a hypoplastic maxilla.Case presentationA 13-year-old Caucasian boy presented with a chief complaint of delayed eruption of the permanent anterior teeth. The patient was subsequently diagnosed with CCD based on the clinical examination, panoramic X-ray, anterior-posterior and lateral cephalogram, and chest radiograph findings. The details of this case are herein reported because of the extremely low incidence of this disorder.ConclusionsCCD is of clinical importance in dentistry and medicine because it affects the bones and teeth and is characterized by many changes in skeletal patterning and growth. Particularly in dentistry, CCD is of great clinical significance because is associated with delayed ossification of the skull sutures, delayed exfoliation of the primary teeth, lack of permanent teeth eruption, multiple supernumerary teeth, and morphological abnormalities of the maxilla and mandible. Patients with CCD seek treatment mainly for dental problems. Knowledge of the pathogenesis, clinical characteristics, and diagnostic tools of CCD will enable clinicians to render the appropriate treatment to improve function and aesthetics. Early diagnosis of CCD is crucial for timely initiation of an appropriate treatment approach.

Non-syndrome patient with bilateral supernumerary teeth: Case report and 9-year follow-up

The presence of supernumerary teeth, also known as hyperdontia, is the condition of having teeth in addition to the regular number of teeth. The occurrence of multiple supernumerary teeth is often found in association with syndromes such as Gardner syndrome, Anderson-Fabry disease, Ellis-van Creveld syndrome, Ehlers-Danlos syndrome, incontinentia pigmenti, and Tricho-rhino-phalangeal syndrome. Only a few examples of nonsyndromic multiple supernumerary teeth have been reported in literature. In this report, we present the unusual case and 9-year follow up of a non-syndrome female patient with bilateral supernumerary teeth that occurred with an interval of several years.

Multiple Supplemental Supernumerary Premolars: Unusual Presentation in a Nonsyndrome Patient

Supplementary teeth in the dental arch are a rare occurrence. Though they are mostly reported in association with syndromes they can also present in the absence of systemic pathology. This paper reports a case with multiple supernumerary teeth along with discussion of the frequency, types, complications, and management of such occurrence.

Imaging in the diagnosis of a rare anomaly: Cleidocranial dysplasia

Cleidocranial dysplasia (CCD) is a rare autosomal dominant and developmental anomaly of skeleton characterized by generalized dysplasia of the bones and teeth. CCD is caused by mutation of transcription factor RuNx2, although 40% of the cases appear spontaneously with no apparent genetic cause. The disorder presents with partial or complete absence of clavicles, open anterior fontanelle, and cranial sutures, presence of multiple wormian bones, short stature, wide pubic symphysis, short middle phalanges of the 5 th finger, over retained deciduous teeth, multiple impacted permanent and supernumerary teeth and various other abnormalities. The frequency of this disorder is one/million individuals. Early diagnosis of CCD is essential for initiating the appropriate treatment approach. In confirmed cases, genetic counseling for family planning should certainly be advised. Because of its rarity, we report the classical case of CCD, with an emphasis on the importance of clinical and radiographic findings.

Late Developing Supernumerary Premolars: Reports of Two Cases

This paper presents two cases of late developing supernumerary premolars. Case 1 is a female patient with nonsyndromic multiple supernumerary teeth located in the maxillary right premolar-molar region, maxillary left premolar region, and the mandibular right and left premolar regions. In this patient surgical removal of all supernumerary teeth was carried out to avoid complications during orthodontic treatment. Case 2 is a female aged 19 years in whom formation of a mandibular supernumerary premolar was observed which was not present at age 13. The patient was made aware of the supernumerary tooth presence, and periodic radiographic assessment was planned.

Nonsyndromic Bilateral Multiple Impacted Supernumerary Mandibular Third Molars: A Rare and Unusual Case Report

A supernumerary tooth is that which is present additionally to the normal series and can be found in any region of the dental arch. An impacted tooth is defined as the one which is embedded in the alveolus, so that its eruption is prevented, or the tooth is locked in position by bone or the adjacent teeth. The occurrence of multiple supernumerary teeth in only one patient in the absence of an associated systemic condition or syndrome is considered as a rare phenomenon. The occurrence of supernumerary teeth in the lower molar region is rare. A prevalence of less than 2% of cases occurring in this region has been estimated. Their occurrence presents a clinical problem for orthodontists and oral surgeons. The cause, frequency, complications, and surgical operation of impacted teeth are always interesting subjects for study and research. An impacted tooth can result in caries, pulp disease, periapical and periodontal disease, temporomandibular joint disorder, infection of the fascial space, root resorption of the adjacent tooth, and even oral and maxillofacial tumours. The management of impacted wisdom teeth has changed over the past 20 years from removal of nonsymptomatic third molars to simple observation. The aim of this paper is to present a rare case of bilateral multiple impacted supernumerary mandibular third molars.

Orthodontic management of non-syndromic multiple supernumerary teeth

Hyperdontia amounts to an odontostomatologic anomaly wherein, there is an increase in tooth number irrespective of the location. This case report represents a form of hyperdontia characterized by bilateral multiple supernumerary teeth in both the jaws without any evident familial history.

A Rare Case of Multiple Oblique Facial Clefts with Supernumerary Teeth: Case Report

Oblique facial clefts are rare congenital anomalies that can present alone or in association with other craniofacial anomalies. A high degree of clefting in the embryo may lead to hyperdontia secondary to dichotomy of the dental lamina. Multiple facial clefts with hyperdontia are clinically challenging and demand comprehensive rehabilitation. This article reports a case of multiple oblique facial clefts of variable severity with multiple supernumerary teeth in a 12-year-old boy. The varied clinical presentation along with the rarity of the occurrence mandate documentation.

Clinical and radiological manifestations of cleidocranial dysplasia: A case report

Cleidocranial dysplasia is a rare hereditary disorder affecting bones and teeth. It can be inherited or can arise spontaneously. It is usually caused by a mutation in the Runx2 gene located on 6p21 chromosome. CCD is associated with complete absence or hypoplasia of the clavicles, delayed or deficient closure of the fontanellas and open sutures, retarded exfoliation of the deciduous teeth, retarded eruption of the permanent teeth and multiple impacted supernumerary teeth. Clinical and radiographic examination display abnormalities of bone and teeth. The main aim of this study is to discuss the diagnostic tools, clinical and genetic features of this disorder and review the literature. Radiographs of skull, teeth, clavicle and pelvis were the diagnostic evidences of our case.

Cleidocranial Dysplasia: A Rare Cause of Disproportionate Severe Short Stature

Skeletal dysplasia is an uncommon cause of short stature in children. An 11-year-old girl was evaluated for severe short stature in a tertiary care hospital. Clinical examination revealed severe disproportionate short stature and classical triad of multiple supernumerary teeth, and complete absence of clavicles and open sagittal sutures and fontanelles. Skeletal survey confirmed these findings, in addition to other features associated with the syndrome.

Mandibular bilateral unerupted non-obstructing supernumerary premolars as a rare paradental anomaly

AbstractNon-syndromal multiple supernumerary teeth are most commonly seen in mandibular premolars region, followed by the molar and the anterior regions respectively. Dental literature rarely reports symmetrical supernumerary teeth in all four quadrants. However, supernumerary premolars may not become radiographically visible until the patient′s normal premolars have erupted. This article presents a case of a 45-year-old male with bilateral unerupted fully formed, buccally angulated, supernumerary premolars in the mandibular region without any obstruction to the eruption of mandibular first and second premolars. There was no syndrome associated. The delayed development of the supernumerary teeth in the premolar region supports the hypothesis that these teeth were part of a post-permanent dentition.

An unusual presentation of generalized aggressive periodontitis with multiple impacted supernumerary teeth

Aggressive periodontitis is a rare condition that progresses rapidly but affects only a small percentage of population. Most of the cases are familial. The presence of supernumerary teeth is also rather rare and often familial. Therefore, a concomitant presentation of aggressive periodontitis and supernumerary teeth in an individual has generated a great interest among clinicians. Here, we report a rare nonsyndromic case of generalized aggressive periodontitis with multiple impacted supernumerary teeth.