AbstractSince the advent of the widespread use of the operating microscope and the excellent graduate and post‐graduate training in otology, more and more otosurgeons are exploring disease of the middle and inner ear; consequently, more and more unusual and varied anomalies and tumors are being described. This paper describes the unusual presentation of acoustic neurinomas in the middle ear.Most acoustic nerve tumors arise within the meatus of the internal auditory canal, producing the syndrome of the cerebellopontine angle.In the first case presented, the tumor did not arise in the usual location, and this points out the fact that acoustic nerve tumors may arise anywhere along the course of the VIIIth nerve. It is felt that the tumor must have arisen in one of the smaller branches of the inferior vestibular nerve, lateral to the vestibule, as it did not extend medially beyond the medial wall of the vestibule. Instead, it presented in the cochlear windows as a middle ear tumor.In the second case, the tumor apparently arose in the usual location, in the meatus of the internal auditory canal. Its lateral extension was unusual, in that the tumor filled the entire labyrinth and presented as a middle ear tumor in the cochlear windows of the middle ear, and its extension medially, produced the classical findings of the cerebellopontine angle tumor.