It is currently accepted that the reproductive capabilities of deaf people increase over time, and marriages between deaf people occur according to the principle of assortativity, which in total can lead to an increase in the frequency of one major autosomal recessive form of deafness. In this regard, the purpose of this work was to analyze the share and structure of assortative marriages based on deafness in the Republic of Buryatia. The sample of deaf individuals consisted of 201 people (113 female and 88 male) aged from 21 to 77 years (mean age 46.7 ± 7.9 years). For analysis of the marriage structure of deaf people, information was available for 168 marriages. Individuals were considered married if they had a registered marriage and/or if they had common children. An assortative marriage (AM) was a marriage in which both partners were deaf. An AM in which all the children were deaf was considered non-complementary, and an AM in which all the children were hearing was considered complementary. Marriages in which there were both hearing and deaf children were designated as segregating. An analysis of the marriage structure of deaf people showed that the proportion of marriages between deaf individuals in Buryatia is 81.8% (122 out of 149 marriages analyzed), and in 18.2% of cases (27 marriages) marriages were concluded between deaf and hearing people. Among all AM, the share of complementary marriages was 86.9% (106 out of 122), non-complementary - 5.7% (7 out of 122) and segregating 7.3% (9 out of 122). It was revealed that with a high frequency of AM, the marital structure was characterized by a high proportion of complementary and low proportion of non-complementary and segregating AM, which may be explained by the peculiarities of the genetic structure of hereditary forms of hearing loss in the Republic of Buryatia. Keywords: hereditary hearing loss, assortative marriages, sign language, autosomal recessive deafness 1A (DFNB1A), Buryatia.
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