Introduction Turner syndrome (TS) represents one of the most common chromosomal abnormalities in females. It is associated with a wide spectrum of clinical features, such as gonadal dysgenesis and short stature. Short stature in TS is usually not attributed to growth hormone deficiency (GHD). The aim of our study was to report 4 cases with TS and GHD. Methodology It is a retrospective study including 4 patients with TS. GHD was confirmed by failure of GH to raise more than 10 ng/mL after L-dopa stimulating test and insulin induced hypoglycemia test. Results All patients were referred to our department with a delayed puberty and short stature. The mean age at the diagnosis of TS was 18.5 ± 2.4 years. Physical examination revealed dysmorphic syndrome in all patients. The mean height was 1.37 ± 0.06 m ( Conclusion GHD is not a common finding in patients with TS. It should be considered only when the short stature is lower than that usually found in TS.