Congenital diaphragmatic hernia (CDH) is characterized by a closure defect in the diaphragm. Many patients’ present signs and symptoms at birth, but late manifestation may occur, making a difficult diagnosis due to a variable clinical condition. Surgery is necessary and the prognosis in the late presentation is favorable when compared to the early manifestation. We will report a case of a male infant, 7 months and 24 days old, with a history of recurrent dyspnea for 15 days, crying a lot, groaning and constipated. After chest radiography and confirmed by chest tomography, the presence of diaphragmatic hernia was confirmed. The surgery was performed and the patient was released after 7 days of hospitalization. In the face of an unusual late diagnosis, it is expected that such information corroborates the importance of the early diagnosis of CDH.