Case Reports1 February 1940A CASE OF ACUTE IDIOPATHIC HEMATOPORPHYRIA WITH ACUTE ASCENDING PARALYSISHAROLD W. PALMER, M.D., F.A.C.P.HAROLD W. PALMER, M.D., F.A.C.P.Search for more papers by this authorAuthor, Article, and Disclosure Informationhttps://doi.org/10.7326/0003-4819-13-8-1500 SectionsAboutPDF ToolsAdd to favoritesDownload CitationsTrack CitationsPermissions ShareFacebookTwitterLinkedInRedditEmail ExcerptIn 1911, in his original monograph, Günther1described a rare constitutional disturbance which he called hematoporphyria, the essential symptom of which was the finding of large quantities of hematoporphyrin in the urine. He later made the statement, confirmed by Hoppe-Seyler, that hematoporphyrin was not the pigment found in the urine in this disease, but that the pigments actually were copraporphyrin and uroporphyrin, related substances. However, through general acceptance by Garrod and others, the pigment is still referred to as hematoporphyrin and the disease state as hematoporphyria. In 1925 Günther1attempted to classify the hematoporphyria into three separate groups, namely, (1)...Bibliography1. GÜNTHER H: Die Bedeutung der Hämatoporphyrine in Physiologie und Pathologie, 1922, J. F. Bergmann, München. CrossrefGoogle Scholar2. MASONFARNHAM VRRM: Acute hematoporphyria, Arch. Int. Med., 1931, xlvii, 467. CrossrefGoogle Scholar3. TURNER WJ: Studies on porphyria, Arch. Int. Med., 1938, lxi, 762-773. CrossrefGoogle Scholar4. MASONCOURVILLEZISKIND VRCE: Porphyrins in human disease, Medicine, 1933, xii, 355-439. CrossrefGoogle Scholar5. COURVILLEMASON CVR: Acute ascending paralysis (Landry's paralysis) with acute idiopathic hematoporphyria, Arch. Neurol. and Psychiat., 1931, xxv, 848-854. CrossrefGoogle Scholar6. DRAKE RL: Acute ascending paralysis (Landry's paralysis), Med. Rec., 1935, cxlii, 232-235. Google Scholar7. WALDENSTRÖM JM: Some observations on acute porphyria and other conditions with a change in the excretion of porphyrins, Acta med. Scand., 1934, lxxxiii, 281-316. Google Scholar8. ROTHMAN PE: Hematoporphyrinuria, Am. Jr. Dis. Child., 1926, xxxii, 219-225. CrossrefGoogle Scholar9. SATOTAKAHOSHI AH: A new form of congenital hematoporphyria; oligochomemia porphyrinuria (megalosplenica congenita), Am. Jr. Dis. Child., 1926, xxxii, 325-333. Google Scholar10. KALDEWEY W: Landrysche Paralyse, Porphyrie, Sulfonal, Ztschr. f. d. ges. Neurol. u. Psychiat., 1933, cxlv, 165-184. CrossrefGoogle Scholar11. GOECKERMANOSTERBERGSHEARD WHAEC: Eczema solare in a case of hematoporphyrinuria, Arch. Dermat. and Syph., 1929, xx, 501-505. CrossrefGoogle Scholar12. BLUMSCHUMACHER HFIC: Abnormal sensitivity to light in a case of possible Landry's paralysis, ANN. INT. MED., 1937, xi, 548-557. Google Scholar This content is PDF only. To continue reading please click on the PDF icon. Author, Article, and Disclosure InformationAffiliations: Wichita, Kansas*Received for publication October 8, 1938.From the departments of Medicine and Pathology, Wichita Hospital, Wichita, Kansas.I wish to express my gratitude to Dr. C. A. Hellwig, Chief of Pathological Service, St. Francis Hospital, Wichita, Kansas, for his very able assistance and advice in the study of the histopathology in this case. PreviousarticleNextarticle Advertisement FiguresReferencesRelatedDetails Metrics Cited byLiteraturverzeichnisErkrankungen der peripheren NervenACUTE PORPHYRIA : A STUDY OF SIX CASESACUTE PORPHYRIA*ALLAN M. GOLDMAN, M.D., F.A.C.P., MURREL H. KAPLAN, M.D., F.A.C.P.ACUTE PORPHYRIA WITH SPINAL FLUID CHANGES*HAROLD A. LYONSACUTE PORPHYRIA 1 February 1940Volume 13, Issue 8Page: 1500-1508KeywordsGratitudeHistopathologyHospital medicineParalysisUrine Issue Published: 1 February 1940 PDF downloadLoading ...