Focusing on the positive outcomes of Caesarean myomectomy, we present a case of successful Caesarean myomectomy in a patient with a huge myoma larger than 10 cm and spontaneous normal pregnancy with a bicornuate uterus. A 38-year-old woman, parity 0-0-0-0, at 36W 2D of gestation, with a known bicornuate uterus was admitted at our Hospital with bloody show. Under a spinal anesthesia block, a Caesarean section was performed. The transverse myometrial incision was made, then, the baby was delivered from the hip under gentle guidance. A male viable baby weighing 2240 g was delivered with transverse presentation on the right uterine cavity. The Apgar scores were 5 and 8 at 1 and 5 minutes. The uterus was closed according to the standard protocol, and the intramural myoma in the anterior body was removed. Before removing the myoma capsule, vasopressin injection was administered to reduce the myoma blood supply as much as possible, a longitudinal incision was made, after myomectomy, an open space was closed with interrupted sutures. To prevent hemorrhage, continuous IV oxytocin and methylergonovine were added for 3 days after the surgery. During surgery, the blood loss volume was 1 L, and the postoperative day 3 hemoglobulin level was 11.7 g/dL, with stable vital signs. The patient was discharged after 5 days of admission without specific surgical complications. During 8 weeks of postoperative follow-up, satisfactory progress was observed without additional complications. Our hospital is a tertiary medical institute with attending obstetricians with >10 years of experience. Therefore, over the last 9 years, we performed Caesarean myomectomy. For every surgery, the feasibility of performing Caesarean myomectomy is always considered, and most cases have been successful, with no significant increase in morbidity. Thus, we performed a huge myomectomy for a uterine malformation, with a satisfactory result. Please note: The publisher is not responsible for the content or functionality of any supporting information supplied by the authors. Any queries (other than missing content) should be directed to the corresponding author for the article.