Case Of Dysplasia Epiphysealis Hemimelica Research Articles

Dysplasia Epiphysealis Hemimelica

Summary: A new case of dysplasia epiphysealis hemimelica is reported. It is the third case reported in Spain and presents involvement of almost all the epiphyses of the left side of the body. The involvement of the left hip following surgery is hard to explain. The patient also presents lengthening of the left lower limb. Following a review of the world literature, it seems that this case demonstrates the greatest epiphyseal involvement to date.

Dysplasia Epiphysealis Hemimelica

Fifteen new cases of dysplasia epiphysealis hemimelica are reported and the literature is reviewed. The cartilage overgrowth was usually found to be limited to one extremity and to half of the affected epiphysis. The microscopic pathological changes are indistinguishable from those of an osteocartilaginous exostosis. Excision of the lesion is indicated when it produces deformity or interferes with function. Other procedures are seldom required. These lesions retain the potential for cartilage proliferation in adult life and, we presume, for malignant degeneration. They should be closely followed in the adult and be removed if they increase in size.

Dysplasia epiphysialis hemimelica (tarso-ephiphysial aclasis).

Dysplasia epiphysialis hemimelica (tarso-ephiphysial aclasis).