Y-type urethral duplication with posterior perineal fistula: A new variant

Sandesh V Parelkar,Beejal Sanghvi,Arjun Apparao Pawar,Rahul Kumar Gupta

doi:10.14534/pucr.2017327012

Sandesh V Parelkar, Beejal Sanghvi + Show 2 more

Open Access

https://doi.org/10.14534/pucr.2017327012

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Abstract

13 months old boy presented with constipation and straining during micturition with poor urinary stream and voiding of urine per rectum. Perineal examination revealed posterior perineal fistula. Voiding cysto-urethrogram showed bilateral vesicoureteral reflux with bladder diverticuli, normal dorsal urethra and dye going from urethra to rectum suggestive of Y type urethral duplication. Under stoma cover, he underwent excision of posterior perineal fistula with accessory ventral urethra and anorectoplasty was done. At present patient is passing urine in good stream without straining. The uniqueness of our case is the presence of Y type of urethral duplication with normal calibre dorsal urethra and presence of posterior perineal fistula. Therefore, we consider our case to be an unusual variant of Y type of urethral duplication that has not been described before.

Highlights

We present an unusual case of Y type urethral duplication with normal calibre dorsal urethra associated with posterior perineal fistula
Urethral duplication is a rare anomaly usually seen in males, Y type of urethral duplication is often associated with low anorectal malformations; in the form of anal stenosis of normally or slightly anteriorly placed anal opening
High sigmoid colostomy was done in view of Y type urethral duplication with posterior perineal fistula

Summary

Introduction

We present an unusual case of Y type urethral duplication with normal calibre dorsal urethra associated with posterior perineal fistula. Introduction Urethral duplication is a rare anomaly usually seen in males, Y type of urethral duplication is often associated with low anorectal malformations; in the form of anal stenosis of normally or slightly anteriorly placed anal opening. High sigmoid colostomy was done in view of Y type urethral duplication with posterior perineal fistula.

Results

Conclusion