Abstract
Introduction: Hemangiopericytoma is a rare vascular tumor representing about 1% of all vascular tumors and approximatively 5% of all soft tissues sarcomas that arises from the pericytes of Zimmerman surrounding capillaries and postcapillaries vessels. Retroperitoneal hemangiopericytomas are rare among the localisations as it usually occurs in lower and upper extremities.Presentation of case: We present a case of 31-year-old man with a well-defined retro peritoneal mass measuring about 105 × 73 × 83 mm at right lower quadrant of the abdomen anterior to right psoas muscle. Intraoperatively, an large mass measuring 10 × 8 cm was found arising from the retro peritoneum. A monobloc excision was performed. The postoperative course was uneventful. Histopathological examination with immune histochemistry revealed that tumoral cells were positive for desmin, CD34, smooth muscular antigen. Final diagnosis of hemangiopericytoma was made. On the last follow up at one year, he was symptom free.Discussion: Hemangiopericytoma is a rare tumor. It takes origin from pericytes presenting as intervals along the walls of capillaries and post-capillary venules. Retroperitoneal hemangiopericytoma is a rare location. It is often discovered at late course, and can be revealed by various symptoms with the compression of the adjacent organs by the tumor Surgical resection should be considered in symptomatic cases or in case of diagnostic dilemma.Conclusion: Retroperitoneal hemangiopericytoma can be benign but it should be treated the same way as aggressive tumors. It requires a careful and long term follow up.
Highlights
Hemangiopericytoma is a rare vascular tumor representing about 1% of all vascular tumors and approximatively 5% of all soft tissues sarcomas [1] that arise from the pericytes of Zimmerman surrounding capillaries and postcapillaries vessels
The guidelines in terms of management of retroperitoneal hemangiopericytomas were established on the basis of case reports and case series and some aspects
We report a case of retroperitoneal hemangiopericytoma in an adult treated successfully by a monobloc excision
Summary
Hemangiopericytoma is a rare vascular tumor representing about 1% of all vascular tumors and approximatively 5% of all soft tissues sarcomas [1] that arise from the pericytes of Zimmerman surrounding capillaries and postcapillaries vessels. Retroperitoneal hemangiopericytomas are rare among the localisations as it usually occurs in lower and upper extremities [2]. The rarity of these tumors makes the understanding for the pathologic radiologic findings difficult the progresses made in the level of the sensivity of the new imaging techniques. The guidelines in terms of management of retroperitoneal hemangiopericytomas were established on the basis of case reports and case series and some aspects. We report a case of retroperitoneal hemangiopericytoma in an adult treated successfully by a monobloc excision. This case has been reported in line with the SCARE criteria [3]
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