Untreated Craniostenosis causing severe Mental retardation with X-ray skull showing Silver beaten appearance skull on: Role of physician in early diagnosis and surgical Management

Guru Dutta Satyarthee,Satyajit Panda

doi:10.15761/gimci.1000135

Abstract

Untreated Craniostenosis causing severe Mental retardation with X-ray skull showing Silver beaten appearance skull on: Role of physician in early diagnosis and surgical Management

Highlights

Craniostenosis is characterized by early fission of sutures of skull, when premature closure of the sagittal suture occurs called as Scaphocephaly [1]
Neglected cases can develop typical scaphoid appearance of head and silver beaten appearance or known as beaten brass skull, refers to the prominence of gyral impressions on the inner table of the skull observed throughout the skull vault and typically associated with raised intracranial pressure in children [3,4,5]
Every case of craniostenosis should be subjected to surgical intervention at as early as possible preferably within first three months of infancy to protect from bad effect of raised Intracrnial pressure [6,7,8]

Summary

Introduction

Craniostenosis is characterized by early fission of sutures of skull, when premature closure of the sagittal suture occurs called as Scaphocephaly [1]. It causes arrest of growth of brain and causes deformity of skull along with features of raised intracranial pressure. A 7-year–old-male boy presented to our outpatient clinic with complaints of abnormal shape of head along with abnormal facial profile. He was mentally subnormal and had abnormal protrusion of both eyes associated with bilateral progressive diminution of vision. Patient had uneventful post-operative course and was doing well at follow-up visit six months after surgery

Discussion

Conclusion