Abstract
Steroid cell tumour of the ovary is a very rare sex cord stromal tumour of ovary which commonly presents in women belonging to third and fourth decade of life. It usually manifests with a pelvic mass along with androgenic symptoms. We present a case of 3 year old child, who presented with precocious puberty and hirsutism. Radiology was suggestive of ovarian mass for which oophorectomy was done. Gross, histopathological examination and immunohistochemistry proved it to be a steroid cell tumour, not otherwise specified. Our case being unique because of presentation at merely 3 years of age.
Highlights
Steroid cell tumor of the ovary is a very rare ovarian neoplasm accounting for only 0.1% of all the ovarian tumors. [1,2] The mean age of presentation is usually 43 years though it reported at a young age
Serum cortisol level and alpha feto protein (AFP) levels were within normal range i.e. 10.78 microgram/deciliter and 3.26 IU/ml respectively
[3] This tumour usually secretes hormones like androstenedione, α-hydroxyprogesterone, and testosterone and shows androgenic manifestations like hirsutism and menstrual irregularities in postmenopausal and younger women and early development of secondary sexual characters i.e. precocious puberty in children. [1,4,9,11] In our case the patient presented with vaginal bleeding, hirsutism and development of axilllary and pubic hair along with abdomino pelvic mass
Summary
Steroid cell tumor of the ovary is a very rare ovarian neoplasm accounting for only 0.1% of all the ovarian tumors. [1,2] The mean age of presentation is usually 43 years though it reported at a young age. [1] To the best of our knowledge, only 24 cases have been reported in literature of steroid cell tumor occurring in young age ranging from 2 to 12 years. [3] The subtype, not otherwise specified is a sex hormone secreting variety with commonly androgenic manifestations.[1,4,9,10,11] Here we present a case of a 3 year old girl who presented with complaints of abdominal pain, hirsutism, vaginal bleeding and development of secondary sexual features. [1] To the best of our knowledge, only 24 cases have been reported in literature of steroid cell tumor occurring in young age ranging from 2 to 12 years. [3] The subtype, not otherwise specified is a sex hormone secreting variety with commonly androgenic manifestations.[1,4,9,10,11] Here we present a case of a 3 year old girl who presented with complaints of abdominal pain, hirsutism, vaginal bleeding and development of secondary sexual features. A 3 year old girl was brought to the outpatient department with complaints of abdominal pain, vaginal bleeding and early development of breast, pubic and axillary hair since 2 months. On Ultrasound examination a right adnexal mass measuring 7.3x6.2x4.3 cm was noted. The final diagnosis was given as steroid cell tumour of right ovary
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