Sprengel’s deformity of the shoulder: A Case report

Abstract

Congenital elevation of the scapula i.e. ‘Sprengel’s shoulder’ is a congenital anomaly of the shoulder girdle that is associated with abnormal descent, and malrotation of the scapula.Conventional anteroposterior radiography of the chest including both shoulders along with CT or MRI is required for diagnosis and proper management. Most common therapeutic choice is surgical intervention for cosmetic and functional recovery of the shoulder. Surgical procedure: With the patient in prone position, in general anaesthesia, Skin incision was given paraspinal area, along superior-medial angle and medial border of the left scapula. After detaching supraspinatus muscle from the scapula along with its periosteum, omovertebral bar was excised, leaving remnant at the connection from the spinous process of c3 vertebra. Then muscles were reattached to the scapula in corrected position. Result: As follow-up after 6 weeks, the patient’s active range of motions improved. Forward flexion was improved from 60° pre-operatively to 120° at six months follow-ups. Similarly abduction improved from 60° to 130°, internal rotation from 15° to 20° and external rotation 0° to 30°. Neurovascular evaluation was within normal limits. X-rays confirmed the position of scapula about 3 cm lower than the pre-operative position which is less than 1 cm higher as compare to right scapula.