SOLID PSEUDOPAPILLARY TUMOR OF THE PANCREAS IN CHILDREN: 10 YEARS OF EXPERIENCE

Abstract

Introduction: a solid pseudopapillary tumor (SPPT) of the pancreas is an extremely rare disease occurring in 0.13-2.7% of all pancreatic tumors. This tumor is characterized by a fairly favorable clinical course, with low metastasis potential. The clinical picture is highly non-specific, it is more common in girls of puberty and young women under 30 years of age. The main treatment method is surgical. The purpose of the study is to study the clinical and pathological characteristics of this disease and the possibilities of surgical treatment of patients with this pathology. Material and methods. The analysis of clinical data of patients diagnosed with SPPT in our Institute over the past 10 years (2007-2017). And also therу was reviewed the morphological data of SPPT, types of surgical treatment, results, and complications. Results. For 10 years, SPPT was detected in 24 patients. All patients were girls of puberty from 9 to 17 years. In most cases, the disease was asymptomatic and was diagnosed as an "accidental find" during a medical examination. Two patients had liver metastases. All patients underwent surgical treatment in a different volume: 8 patients - laparoscopic distal pancreatic resection, 3 - gastropancreatoduodenal resections, 3 - pancreatoduodenal resection, 6 - central pancreatic resections, 3 - distal subtotal pancreas resection and 1 - resection of uncinate process of the pancreas with resection of the duodenal wall. Complications occurred in 6 patients: in 4 - postoperative pancreatitis with the formation of pancreatic fistula and in one case - bleeding from the pancreatic branch of the splenic artery and bleeding from the wound surface. The follow-up period lasted from 3 months to 11 years. All patients are alive. Conclusion. SPPT is a rare tumor with a benign course potential. Clinical signs and symptoms are relatively nonspecific. Surgical treatment is the main method of treatment, although it is characterized by a high risk of postoperative complications. In general, the prognosis of this disease is favorable, even in the presence of distant metastases.