Single coronary ostium, unilateral pulmonary atresia and MAPCA with tetralogy of fallot in a young adult: a rare association

Abstract

Tetralogy of Fallot (TOF) is the most common form of cyanotic congenital heart disease (CHD). The mortality rate in untreated patients reaches 50% by age 6 years. It is also the most common form of cyanotic CHD with survival upto adulthood. However, TOF with both coronary and pulmonary vasculature anomalies is an extreme variant. We report a case of TOF with single coronary ostium (SCA); atretic branch pulmonary arteries and major aortopulmonary collateral artery (MAPCA) with relatively symptomless period upto 22 years of age.