Abstract
ABSTRACTWorld Health Organization (WHO) blue book of head and neck tumors reports 64 cases of ameloblastic fibrosarcoma and 14 cases of ameloblastic fibrodentinosarcoma/fibro-odontosarcoma. We present a unique case that does not fit into any of the WHO classified odontogenic sarcomas. The patient presented in 2006 with a densely sclerotic lesion arising from the left sphenoid bone, displacing the orbital contents and extending up to the inferior margin of the maxillary sinus. He was treated with left maxillectomy orbital exenteration. He relapsed 6 years later, salvage surgery was unsuccessful and subsequent care was supportive. Histologically the malignant neoplasm showed follicles comprising of peripheral columnar cells lined up in palisaded fashion with hyperchromatic nuclei displaced away from basement membrane. Center of the follicles comprised of spindle-shaped cells resembling stellate reticulum. Intervening areas showed fibrosarcomatous areas. Other areas revealed predominant sheets of round cells having hyperchromatic nuclei, inconspicuous nucleoli and scant cytoplasm. These round cells revealed strong membranous positivity for CD99.How to cite this articleHussain R, Hassan U, Jamshed A, Loya A. Round Blue Cell Tumor arising in the Background of Ameloblastic Fibrosarcoma. Int J Head Neck Surg 2013;4(2): 83-85.
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