Reverse straatsma syndrome and lamellar cataract: a case report and review of the literature

Abstract

Myelinated retinal nerve fiber (MRNF) is a developmental anomaly that is often detected during routine ophthalmological examination, but can be an ocular finding in a wide variety of diseases. An important example of this group is the Straatsma Syndrome. Straatsma Syndrome is an entity that presents with the triad of myopia, amblyopia, and MRNF. When this triad is accompanied by hyperopia instead of myopia, it is referred to as the Reverse Straatsma Syndrome. Here, we present a case of Reverse Straatsma Syndrome accompanied by lamellar congenital cataracts.