Pulmonary Cystic Adenomatoid Malformation, Prenatal Diagnosis and Case Management

González El,Castillo As

doi:10.16966/2689-3096.119

Abstract

The Cystic Adenomatous Malformation (CAM) is a rare fetal lung lesion. Its frequency is about 1 in 4000 births and is characterized by an overgrowth of terminal respiratory bronchioles that forms cysts of various sizes. It can be associated with polyhydramnios and pulmonary hypoplasia. We describe here a case of Adenoid Cystic Pulmonary Malformation type II with prenatal diagnosis at 20 weeks of gestational age, as well as its subsequent management. Morphological ultrasound describes multiple small cysts associated with a slight mediastinal deviation. The prognosis depends mainly on the associated injuries. Prenatal ultrasound allows early diagnosis and follow-up of CCAM to monitor the appearance of possible pathophysiological complications that may worsen its prognosis.

Highlights

Pulmonary Cystic Adenoid Malformation (CCAM) is a rare anomaly in lung development with few cases reported in the world literature
At 24s, a consistent biometry is noticed in the thoracic examination, an echogenic formation is observed at the left lung level of 28 × 24 × 20 mm, with cystic areas inside (Figure 3)
The first description of the Cystic adenomatoid malformation of the lung (CCAM) was made by Chin and Tang in 1949

Summary

Introduction

Pulmonary Cystic Adenoid Malformation (CCAM) is a rare anomaly in lung development with few cases reported in the world literature. It was first described by Bartholinuis in 1687, but was not described in more detail until 1949 by Chin and Tang. Cystic adenomatoid malformation of the lung (CCAM) is an adenomatous proliferation of the terminal bronchioles, with suppression of alveolar growth [1,2]. The diagnosis of CCAM is ultrasound [5] and is usually made at early gestational ages

Materials and Methods

Findings

Discussion and Conclusion