Abstract
Recurrent eccrine syringomatous carcinoma is an extremely rare adnexal tumor predominantly found in the head and neck region. We present a case of a 75-year-old woman with a 7-year history of recurrent syringoid eccrine carcinoma in the scalp and auricle. She had undergone five previous oncologic resections and declined further oncologic ablation of the auricle, including temporal bone and external ear canal resection. We performed five sessions of palliative photodynamic therapy using topical aminolevulinic acid HCL 20% (ALA) and between 25 and 33 pulses of Intense Pulsed Light (Quantum) with an intensity of 30 Joules. The ALA incubation time was 3 hours, while the time between each session was 4 weeks. This treatment helped to control ulceration, pain, and swelling. We saw the patient 1 month after the last treatment, by that time she moved and we lost contact.
Highlights
Syringoid Eccrine carcinoma (SEC) is a very rare tumor
We present a case of a 75-year-old woman with a 7-year history of recurrent syringoid eccrine carcinoma in the scalp and auricle
Most patients survive beyond 10 years and usually die of another cause, notable exceptions of death within 6 months of diagnosis due to metastasis to the lymph nodes and lungs have been reported
Summary
Syringoid Eccrine carcinoma (SEC) is a very rare tumor It is very locally invasive, destructive, and is often recurrent. It was originally described as a basal cell tumor with eccrine differentiation in 1969 [1]. SEC resembles syringoma in its ductal, cystic, and comma-like epithelial components It differs from syringoma in its cellularity, anaplasia, and deep invasiveness [2]. The tumor presents itself in patients ranging from 1 to 86 years of age, with most cases occurring in the fifth to seventh decades of life. Chemotherapy is not commonly used, administration of trastuzumab has been reported in a metastatic tumor with Her2/neu gene amplification [6]
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