Perineal lipoma mimicking an accessory penis with scrotum

Abstract

A case of accessory penis with scrotum in a 4 months old boy is reported because of its rarity. The infant presented with a tumour mimicking an accessory penis with scrotum between the normal sited scrotum and anus. Both testes had descended into the scrotum. After complete evaluation, there was no other urological anomaly. The tumour was excised and the histo-pathological findings of the tumor indicated a perineal lipoma. An overview of normal development of male external genitalia has been provided and the deranged mechanism resulting in this anomaly has been reviewed with hypothesis regarding etiology of accessory scrotum.