Abstract
Purposes: Intralobar pulmonary sequestration is a rare congenital anomaly that causes nonspecific respiratory symptoms. This report presented our surgical experience for pediatric cases of intralobar pulmonary sequestration in our institute. Methods: Between 2002 and 2014, 30 pediatric patients with intralobar pulmonary sequestration underwent lobectomy. The clinical characteristics of patients were retrospectively analyzed using medical records and imaging data. Results: The median age at operation was 23 months. The sequestered lung was situated in the right lower lung in 15 cases and in the left lower lung in 15 cases. Eight cases were prenatally diagnosed by fetal ultrasound and magnetic resonance imaging. One aberrant artery was seen in 26 cases and two aberrant arteries in 4 cases. The drainage vein from the sequestered lung was: 1) the pulmonary vein in 27 cases; 2) the inferior vena cava in 1 case; and 3) the azygos vein and the pulmonary vein in 2 cases. All patients underwent lower lobectomy of the affected side without postoperative early and long-term complications. Conclusion: Due to the increased rate of prenatal diagnoses, the age at operation has decreased. With respect to safety, it is vital to ascertain the number of aberrant arteries and the venous drainage route before lobectomy.
Highlights
IntroductionPulmonary sequestration is a relatively rare congenital lung malformation that accounts for between 0.15% and 6.4% of all congenital pulmonary malformations [1]
Pulmonary sequestration is a relatively rare congenital lung malformation that accounts for between 0.15% and 6.4% of all congenital pulmonary malformations [1]. It is classified into two types, extralobar sequestration (ELS) and intralobar sequestration (ILS)
ELS is separated from normal lung tissue by its visceral pleura, whereas ILS is incorporated within normal lung tissue [2]
Summary
Pulmonary sequestration is a relatively rare congenital lung malformation that accounts for between 0.15% and 6.4% of all congenital pulmonary malformations [1]. It is classified into two types, extralobar sequestration (ELS) and intralobar sequestration (ILS). ELS is separated from normal lung tissue by its visceral pleura, whereas ILS is incorporated within normal lung tissue [2]. In both ILS and ELS, the sequestered lung is supplied by anomalous arteries (aberrant arteries) from the systemic circulation [3]. To ensure safety, it is important to collect comprehensive preoperative information on the site of the sequestered lung, the number of aberrant arteries, and the route of the draining vein
Sign-in/Register to view highlights & summary 
Published Version (
Free)
Talk to us
Join us for a 30 min session where you can share your feedback and ask us any queries you have
Schedule a call