Abstract
A 15-year-old male presented with recurrent, episodic, bilateral eyelid swelling over two days. On examination, he exhibited bilateral eyelid edema, a superotemporal mass, proptosis, and limitation in extraocular motility. Laboratory findings revealed elevated ESR, CRP, and IgG4 serum levels, with negative ANA, ANCA, and ACE. MRI reported symmetrical enlargement of the lacrimal glands with homogeneous enhancement and diffuse restriction. The diagnosis was orbital IgG4-related disease (IgG4-RD) manifesting as bilateral dacryoadenitis, which responded remarkably to systemic steroids. After two years of treatment with immunosuppressants, he experienced no relapses. We share this case to alert clinicians to IgG4-related orbitopathy (IgG4-ROD) in young patients, so that prompt diagnosis and management can be instituted for optimal results.
Published Version
Talk to us
Join us for a 30 min session where you can share your feedback and ask us any queries you have
Schedule a call