P267 Dextrocardia with single ventricle and symptomatic erythrocytosis: a case report

Abstract

Abstract Introduction Dextrocardia is a rare cardiac anomaly which refers to a right-sided location of the heart within the thoracic cavity. Dextrocardia may be associated with other complex cardiac malformations which could result in cyanosis. We reported a case of cyanotic dextrocardia with symptomatic erythrocytosis. Case Report A 54-year-old Asian male was admitted to hospital with the complaint of numbness and tingling of limbs for one month. There was no history of chronic cardio-cerebrovascular diseases or diabetes. On examination vital signs were as follows: blood pressure 112/73 mmHg, pulse 72 beats/min, oxygen saturation 85% on room air, temperature 37.1°C, respiratory rate 18 breaths/min. Cardiac physical examination was indicative of dextrocardia: the apex of the heart was located in the right side of the chest accompanied with a systolic murmur at the apex. Other pertinent examinations showed cyanosis of lips, flushing of face and limbs, and a normal neurological examination. Echocardiography and computed tomography (CT) demonstrated heterotaxy and dextrocardia, normal atriums, common mitral valve, lengthy leaflets of tricuspid valve, dilated single ventricle, double-inlet and outlet left ventricle, mild atrioventricular valve regurgitation (AVVR) and no pulmonary stenosis. Laboratory data showed increased hemoglobin of 19.9 g/dl and hematocrit of 58.8%, decreased oxygen partial pressure of 49.5mmHg and oxygen saturation of 81.3%. The patient was diagnosed with erythrocytosis perhaps secondary to cyanotic congenital heart disease and was given intravenous drip of normal saline to resolute the hyperviscosity status. He refused bone marrow aspiration and surgical evaluation for single-ventricle palliation. During the 16-month follow up, no other symptoms emerged except for mild numbness of limbs. Conclusion Dextrocardia with single ventricle malformation can remain symptom free for a long time until the emergence of complications such as secondary erythrocytosis. It is important to give an early diagnosis and complete evaluation, and echocardiography is an effective method to detect this anomaly. Abstract P267 Figure. The echo and CT images of this case