Ovarian dysgerminoma with abdominal metastasis in a 6-year-old girl

Abstract

Malignant germ cell tumors of the ovary (OGCTs) are rare and represented less than 5% of all germ cell tumors of the ovary. GCTs are composed of several histological types and are divided into two groups: dysgerminomatous germinal malignancies and non-dysgerminomatous germinal malignancies. Ovarian dysgerminomas represented 33% of OGCTs. They can occur at any age but very often in children and adolescents, most often in the second and third decade, rarely in the first decade. The circumstances of discovery are acute abdominal pain, abdominal distension with palpable mass, sometimes we observe menstrual disorders and endocrinological disorders. Imaging findings, ovarian dysgerminoma is presented as a huge solid pelvic mass that can be confused with neuroblastoma which is very common in infants and children. Imaging features with tumor markers permits to confirm the ovarian origin. The Diagnosticof certainty is established by anatomopathological study. These tumors are characterized by a very high chemosensitivity with a better prognosis. We are reporting here a case of ovarian dysgerminoma with abdomino-pelvic metastasis in a 6-year-old girl.